{"orpha":451607,"name":"Cutaneous pseudolymphoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"A rare acquired skin disease characterized by a benign, etiologically variable lymphoproliferative process of the skin mimicking cutaneous lymphoma clinically and/or histologically, while not fulfilling criteria for the diagnosis of a specific disease. Depending on the predominant cell type in the infiltrate, T- and B-cell pseudolymphomas can be distinguished.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-451607/","orphanet_url":"https://www.orpha.net/en/disease/detail/451607","names":{"fr":{"name":"Pseudolymphome cutané","definition":"Maladie dermatologique acquise rare caractérisée par des processus lymphoprolifératifs bénins, de cause variable, simulant cliniquement et/ou histologiquement un lymphome cutané, mais ne répondant pas aux critères de diagnostic d'une maladie spécifique. En fonction du type cellulaire prédominant au sein de l'infiltrat, on peut distinguer les pseudolymphomes T et B."},"de":{"name":"Kutanes Pseudolymphom","definition":"Eine seltene erworbene Hauterkrankung, die durch einen gutartigen, ätiologisch variablen lymphoproliferativen Prozess der Haut gekennzeichnet ist, der klinisch und/oder histologisch ein kutanes Lymphom imitiert, jedoch nicht die Kriterien für die Diagnose einer spezifischen Erkrankung erfüllt. Je nach dem vorherrschenden Zelltyp im Infiltrat können T- und B-Zell-Pseudolymphome unterschieden werden."},"es":{"name":"Pseudolinfoma cutáneo","definition":"Es una enfermedad cutánea adquirida poco frecuente caracterizada por un proceso linfoproliferativo cutáneo, benigno, de etiología variable, simulando clínica y/o histológicamente al linfoma cutáneo, aunque sin cumplir con los criterios diagnósticos de una enfermedad específica. En función del tipo de célula predominante en el infiltrado, se puede diferenciar entre pseudolinfomas de células T y B."},"it":{"name":"Pseudolinfoma cutaneo","definition":"Si tratta di una malattia acquisita rara della cute, caratterizzata da un processo linfoproliferativo benigno, ad eziologia variabile, che interessa la cute e che ricorda, dal punto di vista clinico e/o istologico, il linfoma cutaneo, pur non soddisfacendo i criteri per la diagnosi di una malattia specifica. A seconda del tipo di cellula predominante nell'infiltrato, si distinguono i pseudolinfomi a cellule T e B."},"nl":{"name":"Cutaan pseudolymfoom","definition":"Een zeldzame verworven aandoening van huid, gekarakteriseerd door een goedaardig, etiologisch variabel lymfoproliferatief aanhangsel van de huid dat klinisch en/of histologisch lijkt op cutaan lymfoom, maar niet voldoet aan criteria voor de diagnose van een specifieke ziekte. Afhankelijk van het overheersende celtype in het infiltraat kunnen pseudo-T-cellymfoom en pseudo-B-cellymfoom onderscheiden worden."},"pt":{"name":"Pseudolinfoma cutâneo"},"pl":{"name":"Pseudochłoniak skóry"},"cs":{"name":"Kožní pseudolymfomy"},"uk":{"name":"Шкірна псевдолімфома","definition":"A rare acquired skin disease characterized by a benign, etiologically variable lymphoproliferative process of the skin mimicking cutaneous lymphoma clinically and/or histologically, while not fulfilling criteria for the diagnosis of a specific disease. Depending on the predominant cell type in the infiltrate, T- and B-cell pseudolymphomas can be distinguished."},"zh":{"name":"皮肤假性淋巴瘤"},"tr":{"name":"Kutanöz psödolenfoma"}},"xrefs":[{"source":"ICD-10","code":"L98.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"4A43.0","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1620802923"},{"source":"MONDO","code":"0018680","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0311220","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":284264,"name":"IgG4-related disease","classifications":[196]},{"orpha":90077,"name":"Other acquired skin disease","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult","Elderly"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET_27057027[PMID]"},{"type":"Cases/families","qualification":"Case(s)","class":null,"value":60.0,"area":"Worldwide","status":"Validated","source":"27057027[PMID]"}],"phenotypes":null}