raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:443070

Hemicrania continua

Type
Disease
Group
Disorder
Inheritance
Not applicable
Status
active

A rare trigeminal autonomic cephalalgia characterized by indomethacin-sensitive, persistent, strictly unilateral headache lasting for more than three months, associated with ipsilateral conjunctival injection, lacrimation, nasal congestion, rhinorrhea, forehead and facial sweating, miosis, ptosis, eyelid edema, and/or restlessness or agitation, and not better accounted for by another type of headache. Migrainous symptoms such as photophobia are often observed. The headache may be continuous (unremitting subtype) or interrupted by remission periods of more than 24 hours (remitting subtype).

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enHemicrania continua
frHémicrânie continue
deHemicrania continua
esHemicránea continua
itEmicrania continua
nlHemicrania continua
ptHemicrania continua
plHemikrania ciągła
csHemicrania continua
ukПостійна геморагія
zh连续性半侧颅痛
trHemikrani kontinua

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10G44.0NTBTattributedvalidated
ICD-118A82NTBTindexvalidated
MONDO0018615Evalidated
UMLSC2349425Evalidated
GARD10795Evalidated
MedDRA10090227Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card