raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:439746

Secondary polyarteritis nodosa

Synonyms: Secondary PAN · Secondary periarteritis nodosa

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Status
active

Secondary polyarteritis nodosa (PAN) is a rare serious form of PAN characterized by vasculitis in a background of viral infection, primarily with hepatitis B virus (HBV).

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enSecondary polyarteritis nodosaSecondary PAN · Secondary periarteritis nodosa
frPériartérite noueuse secondairePAN secondaire · Polyartérite noueuse secondaire
deSekundäre Polyarteriitis nodosaPeriarteriitis nodosa, sekundäre · Sekundäre PAN
esPoliarteritis nodosa secundariaPAN secundaria · Periarteritis nodosa secundaria
itPoliarterite nodosa secondariaPAN secondaria · Periarterite nodosa secondaria
nlSecundaire polyarteriitis nodosaSecundaire PAN · Secundaire periarteriitis nodosa
ptPoliarterite nodosa secundária
plWtórne guzkowe zapalenie tętnicSecondary periarteritis nodosa · Wtórne PAN
csSekundární polyarteritis nodosaSekundární PAN · Sekundární periarteritis nodosa
ukВторинний вузликовий поліартеріїтВторинна PAN · Вторинний вузликовий периартеріїт
zh继发性结节性多动脉炎继发性结节性动脉周围炎
trSekonder poliarteritis nodozaSekonder PAN · Sekonder periarterit nodosa

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10M30.0NTBTattributedvalidated
ICD-10M30.8NTBTattributedvalidated
ICD-114A44.4NTBTattributedvalidated
MONDO0018594Evalidated
UMLSC5680050Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

  • ORPHA:767Polyarteritis nodosa
    rare neurological diseases; rare renal diseases; rare systemic and rheumatological diseases; rare circulatory system diseases; rare systemic or rheumatologic diseases of childhood; rare transplant-related disorders

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card