{"orpha":439746,"name":"Secondary polyarteritis nodosa","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Secondary PAN","Secondary periarteritis nodosa"],"definition":"Secondary polyarteritis nodosa (PAN) is a rare serious form of PAN characterized by vasculitis in a background of viral infection, primarily with hepatitis B virus (HBV).","note":null,"url":"https://raremap.alftech.space/d/ORPHA-439746/","orphanet_url":"https://www.orpha.net/en/disease/detail/439746","names":{"fr":{"name":"Périartérite noueuse secondaire","synonyms":["PAN secondaire","Polyartérite noueuse secondaire"],"definition":"Forme rare et sévère de périartérite noueuse caractérisée par une vascularite sur fond d'infection virale, principalement par le virus de l'hépatite&nbsp;B (VHB)."},"de":{"name":"Sekundäre Polyarteriitis nodosa","synonyms":["Periarteriitis nodosa, sekundäre","Sekundäre PAN"]},"es":{"name":"Poliarteritis nodosa secundaria","synonyms":["PAN secundaria","Periarteritis nodosa secundaria"],"definition":"Es una forma grave y poco frecuente de poliarteritis nodosa (PAN) caracterizada por vasculitis en un contexto de infección viral, principalmente por el virus de la hepatitis B (VHB)."},"it":{"name":"Poliarterite nodosa secondaria","synonyms":["PAN secondaria","Periarterite nodosa secondaria"],"definition":"La poliarterite nodosa secondaria (PAN) è una forma grave e rara di PAN (si veda questo termine), caratterizzata da vasculite in presenza di infezione virale, soprattutto da virus dell'epatite B (HBV)."},"nl":{"name":"Secundaire polyarteriitis nodosa","synonyms":["Secundaire PAN","Secundaire periarteriitis nodosa"],"definition":"Secundaire polyarteriitis nodosa (PAN) is een zeldzame, ernstige vorm van PAN (zie deze term) die gekarakteriseerd wordt door vasculitis in de context van virale infectie, voornamelijk met hepatitis B-virus (HBV)."},"pt":{"name":"Poliarterite nodosa secundária"},"pl":{"name":"Wtórne guzkowe zapalenie tętnic","synonyms":["Secondary periarteritis nodosa","Wtórne PAN"]},"cs":{"name":"Sekundární polyarteritis nodosa","synonyms":["Sekundární PAN","Sekundární periarteritis nodosa"]},"uk":{"name":"Вторинний вузликовий поліартеріїт","synonyms":["Вторинна PAN","Вторинний вузликовий периартеріїт"],"definition":"Secondary polyarteritis nodosa (PAN) is a rare serious form of PAN (see this term) characterized by vasculitis in a background of viral infection, primarily with hepatitis B virus (HBV)."},"zh":{"name":"继发性结节性多动脉炎","synonyms":["继发性结节性动脉周围炎"],"definition":"继发性多发性结节性动脉炎（PAN）是一种罕见的严重PAN型（见本术语），其特征是在病毒感染的背景下由乙型肝炎病毒（HBV）引起的血管炎。"},"tr":{"name":"Sekonder poliarteritis nodoza","synonyms":["Sekonder PAN","Sekonder periarterit nodosa"]}},"xrefs":[{"source":"ICD-10","code":"M30.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"M30.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"4A44.4","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0018594","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680050","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":767,"name":"Polyarteritis nodosa","classifications":[181,188,196,198,231,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}