raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:424982

Biliary cystadenocarcinoma

Synonyms: Intrahepatic bile duct cystadenocarcinoma

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enBiliary cystadenocarcinomaIntrahepatic bile duct cystadenocarcinoma
frCystadénocarcinome biliaireCystadénocarcinome hépatobiliaire
deBiliäres Zystadenokarzinom der LeberZystadenokarzinom des intrahepatischen Gallengänge
esCistoadenocarcinoma biliarCistoadenocarcinoma del conducto biliar intrahepático
itCistoadenocarcinoma biliareCistadenocarcinoma delle vie biliari intraepatiche
nlBiliair cystadenocarcinoomCystadenocarcinoom van de intrahepatische galwegen
ptCistoadenocarcinoma biliarCistadenocarcinoma do TBIH
plTorbielogruczolakorak przewodów żółciowychTorbielogruczolakorak wewnątrzwątrobowego przewodu żółciowego
csBiliární cystadenokarcinomCystadenokarcinom intrahepatálních žlučových cest
ukБіліарна цистаденокарциномаВнутрішньопечінкова цистаденокарцинома жовчних проток
zh胆囊囊腺癌肝内胆管囊腺癌
trBiliyer kistadenokarsinomİntrahepatik safra kanalı kistadenokarsinomu
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C22.1NTBTindexvalidated
ICD-112C12.1YNTBTindexvalidated
MONDO0018535Evalidated
UMLSC0334286Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

15 records
TypeClassValueAreaQualificationValidationSource
Annual incidence<1 / 1 000 0000.002 / 100 000EuropeValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.002 / 100 000AustriaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.002 / 100 000BelgiumValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.005 / 100 000BulgariaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.01 / 100 000Czech RepublicValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.009 / 100 000EstoniaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.005 / 100 000FranceValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000GermanyValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000ItalyValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.005 / 100 000LatviaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000NorwayValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.002 / 100 000PortugalValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.009 / 100 000SpainValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.002 / 100 000NetherlandsValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.001 / 100 000United KingdomValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card