{"orpha":424982,"name":"Biliary cystadenocarcinoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Intrahepatic bile duct cystadenocarcinoma"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-424982/","orphanet_url":"https://www.orpha.net/en/disease/detail/424982","names":{"fr":{"name":"Cystadénocarcinome biliaire","synonyms":["Cystadénocarcinome hépatobiliaire"]},"de":{"name":"Biliäres Zystadenokarzinom der Leber","synonyms":["Zystadenokarzinom des intrahepatischen Gallengänge"]},"es":{"name":"Cistoadenocarcinoma biliar","synonyms":["Cistoadenocarcinoma del conducto biliar intrahepático"]},"it":{"name":"Cistoadenocarcinoma biliare","synonyms":["Cistadenocarcinoma delle vie biliari intraepatiche"]},"nl":{"name":"Biliair cystadenocarcinoom","synonyms":["Cystadenocarcinoom van de intrahepatische galwegen"]},"pt":{"name":"Cistoadenocarcinoma biliar","synonyms":["Cistadenocarcinoma do TBIH"]},"pl":{"name":"Torbielogruczolakorak przewodów żółciowych","synonyms":["Torbielogruczolakorak wewnątrzwątrobowego przewodu żółciowego"]},"cs":{"name":"Biliární cystadenokarcinom","synonyms":["Cystadenokarcinom intrahepatálních žlučových cest"]},"uk":{"name":"Біліарна цистаденокарцинома","synonyms":["Внутрішньопечінкова цистаденокарцинома жовчних проток"]},"zh":{"name":"胆囊囊腺癌","synonyms":["肝内胆管囊腺癌"]},"tr":{"name":"Biliyer kistadenokarsinom","synonyms":["İntrahepatik safra kanalı kistadenokarsinomu"]}},"xrefs":[{"source":"ICD-10","code":"C22.1","qualifier":"NTBT","icd_relation":"index","validated":true},{"source":"ICD-11","code":"2C12.1Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1885299196"},{"source":"MONDO","code":"0018535","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0334286","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":424936,"name":"Carcinoma of liver and intrahepatic biliary tract","classifications":[183,202]},{"orpha":506210,"name":"Rare disorder potentially indicated for liver transplant","classifications":[233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.002,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.002,"area":"Austria","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.002,"area":"Belgium","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual 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