Carcinoma of esophagus, salivary gland type
Synonyms: Esophageal carcinoma, salivary gland type
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A rare gastroesophageal tumor characterized by a typically submucosal tumor occurring usually in the middle to distal esophagus and histologically characterized as either mucoepidermoid (intimate mixture of mucus, intermediate, and epidermoid cells) or as adenoid cystic carcinoma (biphasic admixture of duct‐lining epithelial and myoepithelial cells with tubular, cribriform, solid, or basaloid growth patterns). Patients may be asymptomatic or may present with progressive dysphagia, heartburn, retrosternal pain and/or weight loss.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Carcinoma of esophagus, salivary gland type | Esophageal carcinoma, salivary gland type |
| fr | Carcinome de l'oesophage type glande salivaire | |
| de | Ösophaguskarzinom vom Speicheldrüsentyp | Speiseröhrenkrebs vom Speicheldrüsentyp |
| es | Carcinoma de esófago tipo glándulas salivales | Carcinoma esofágico tipo glándulas salivales |
| it | Carcinoma dell'esofago, tipo ghiandola salivare | Carcinoma esofageo, tipo ghiandola salivare |
| nl | Carcinoom van oesofagus, speekselklier-type | Carcinoom van slokdarm, speekselklier-type · Oesofageaal carcinoom, speekselklier-type |
| pt | Carcinoma do esófago, tipo glândulas salivares | |
| pl | Rak przełyku, typ gruczołu ślinowego | = en |
| cs | Karcinom jícnu, typ slinné žlázy | Ezofageální karcinom, typ slinné žlázy |
| uk | Карцинома стравоходу, тип слинної залози | Карцинома стравоходу за типом слинної залози |
| zh | 唾液腺型食管癌 | 唾液腺型食管癌 |
| tr | Yemek borusu karsinomu, tükrük bezi tipi | Özofageal karsinomu, tükrük bezi tipi |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C15.0 | BTNT | attributed | validated |
| ICD-10 | C15.1 | BTNT | attributed | validated |
| ICD-10 | C15.2 | BTNT | attributed | validated |
| ICD-10 | C15.3 | BTNT | attributed | validated |
| ICD-10 | C15.4 | BTNT | attributed | validated |
| ICD-10 | C15.5 | BTNT | attributed | validated |
| ICD-10 | C15.8 | BTNT | attributed | validated |
| ICD-11 | 2B70.Y | NTBT | attributed | validated |
| MONDO | 0018480 | E | validated | |
| UMLS | C5190854 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:70482Carcinoma of esophagus
rare gastroenterological diseases; rare neoplastic diseases
No children.
Codes that Orphanet moved or referred to this one:
- ORPHA:423781OBSOLETE: Carcinoma of stomach, salivary gland type referred to · inactive
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
18 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | 0.004 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.003 / 100 000 | Austria | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.017 / 100 000 | Belgium | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.002 / 100 000 | Bulgaria | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.007 / 100 000 | Czech Republic | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.009 / 100 000 | Estonia | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.002 / 100 000 | Finland | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.004 / 100 000 | Germany | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.009 / 100 000 | Ireland | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.001 / 100 000 | Italy | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.003 / 100 000 | Poland | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.013 / 100 000 | Slovakia | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.006 / 100 000 | Slovenia | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.003 / 100 000 | Spain | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.002 / 100 000 | Netherlands | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.005 / 100 000 | France | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.008 / 100 000 | Portugal | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.004 / 100 000 | United Kingdom | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/418945
- This record as JSON: /data/d/418945.json