ORPHA:399293
Osteonecrosis of the jaw
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
A rare osteonecrosis characterized by an exposed necrotic lesion in the mandible or maxilla present for more than eight weeks, arising as a complication of antiresorptive medication, dental interventions, or trauma and infections. Patients may present with pain, altered neurosensory functions, secondary infections, and (in advanced stages) pathological fractures, or fistulae.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Osteonecrosis of the jaw | |
| fr | Ostéonécrose de la mâchoire | ONM · Ostéochimionécrose de la mâchoire · Ostéochimionécrose maxillaire · Ostéochimionécrose maxillo-mandibulaire · Ostéonécrose des maxillaires · Ostéonécrose maxillaire associée aux biphosphonates |
| de | Osteonekrose des Kiefers | |
| es | Osteonecrosis de la mandíbula | |
| it | Osteonecrosi della mascella | |
| nl | Osteonecrose van kaak | |
| pt | Osteonecrose da mandíbula | |
| pl | Osteonekroza szczęki | |
| cs | Osteonekróza čelisti | |
| uk | Остеонекроз щелепи | |
| zh | 颌骨坏死 | |
| tr | Çene osteonekrozu |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | K10.2 | NTBT | index | validated |
| ICD-11 | DA06.0 | NTBT | index | validated |
| MONDO | 0018378 | E | validated | |
| UMLS | C2711248 | E | validated | |
| MedDRA | 10064658 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:399169Secondary avascular necrosis
rare systemic and rheumatological diseases; rare bone diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/399293
- This record as JSON: /data/d/399293.json