raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:391504

Transient neonatal myasthenia gravis

Synonyms: NMG · Neonatal myasthenia gravis · Transient neonatal acquired myasthenia · Transient neonatal autoimmune myasthenia gravis

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Antenatal, Neonatal
Status
active

Transient neonatal myasthenia gravis (MG) is a rare form of MG occurring in neonates born to mothers who have the disorder or specific circulating autoantibodies.

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Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enTransient neonatal myasthenia gravisNMG · Neonatal myasthenia gravis · Transient neonatal acquired myasthenia · Transient neonatal autoimmune myasthenia gravis
frMyasthénie auto-immune transitoire du nouveau-néMyasthenia gravis transitoire du nouveau-né · Myasthénie acquise transitoire du nouveau-né · Myasthénie auto-immune du nouveau-né · NMG
deTransiente neonatale Myasthenia gravisMyasthenie, erworbene neonatale transiente · NMG · Neonatale Myasthenia gravis · Neonatale autoimmune Myasthenia gravis, transiente Form
esMiastenia grave neonatal transitoriaMiastenia grave autoinmune neonatal transitoria · Miastenia grave neonatal · Miastenia neonatal transitoria adquirida · NMG
itMiastenia gravis neonatale transitoriaMiastenia acquisita neonatale transitoria · Miastenia grave autoimmune neonatale transitoria · Miastenia gravis neonatale · NMG
nlVoorbijgaande neonatale myasthenia gravisNMG · Neonatale myasthenia gravis · Voorbijgaande neonatale auto-immune myasthenia gravis · Voorbijgaande neonatale verworven myasthenie
ptMiastenia gravis neonatal transitória
plMiastenia przejściowa noworodkówAutoimmunologiczna miastenia przejściowa noworodków · Miastenia noworodkowa · Nabyta miastenia przejściowa noworodków · NMG
csTranzientní neonatální myasthenia gravisNMG · Neonatální myasthenia gravis · Tranzientní neonatální získaná myastenie · Tranzientní neonatální autoimunitní myasthenia gravis
ukТранзиторна неонатальна miastenia gravisНеонатальна міастенія · NMG · Транзиторна неонатальна набута міастенія · Транзиторна неонатальна аутоімунна міастенія
zh新生儿短暂性重症肌无力新生儿获得性自身免疫性重症肌无力
trGeçici yenidoğan myastenia gravisNMG · Yenidoğan miyastenia gravisi · Geçici edinsel yenidoğan miyasteni · Geçici yenidoğan otoimmün miyastenia gravis

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10P94.0Especificvalidated
ICD-11KB08.0Especificvalidated
MONDO0018326Evalidated
UMLSC0495465Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

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Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

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Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

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HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

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Sources for this card