Transient neonatal myasthenia gravis
Synonyms: NMG · Neonatal myasthenia gravis · Transient neonatal acquired myasthenia · Transient neonatal autoimmune myasthenia gravis
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- Antenatal, Neonatal
- Status
- active
Transient neonatal myasthenia gravis (MG) is a rare form of MG occurring in neonates born to mothers who have the disorder or specific circulating autoantibodies.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Transient neonatal myasthenia gravis | NMG · Neonatal myasthenia gravis · Transient neonatal acquired myasthenia · Transient neonatal autoimmune myasthenia gravis |
| fr | Myasthénie auto-immune transitoire du nouveau-né | Myasthenia gravis transitoire du nouveau-né · Myasthénie acquise transitoire du nouveau-né · Myasthénie auto-immune du nouveau-né · NMG |
| de | Transiente neonatale Myasthenia gravis | Myasthenie, erworbene neonatale transiente · NMG · Neonatale Myasthenia gravis · Neonatale autoimmune Myasthenia gravis, transiente Form |
| es | Miastenia grave neonatal transitoria | Miastenia grave autoinmune neonatal transitoria · Miastenia grave neonatal · Miastenia neonatal transitoria adquirida · NMG |
| it | Miastenia gravis neonatale transitoria | Miastenia acquisita neonatale transitoria · Miastenia grave autoimmune neonatale transitoria · Miastenia gravis neonatale · NMG |
| nl | Voorbijgaande neonatale myasthenia gravis | NMG · Neonatale myasthenia gravis · Voorbijgaande neonatale auto-immune myasthenia gravis · Voorbijgaande neonatale verworven myasthenie |
| pt | Miastenia gravis neonatal transitória | |
| pl | Miastenia przejściowa noworodków | Autoimmunologiczna miastenia przejściowa noworodków · Miastenia noworodkowa · Nabyta miastenia przejściowa noworodków · NMG |
| cs | Tranzientní neonatální myasthenia gravis | NMG · Neonatální myasthenia gravis · Tranzientní neonatální získaná myastenie · Tranzientní neonatální autoimunitní myasthenia gravis |
| uk | Транзиторна неонатальна miastenia gravis | Неонатальна міастенія · NMG · Транзиторна неонатальна набута міастенія · Транзиторна неонатальна аутоімунна міастенія |
| zh | 新生儿短暂性重症肌无力 | 新生儿获得性自身免疫性重症肌无力 |
| tr | Geçici yenidoğan myastenia gravis | NMG · Yenidoğan miyastenia gravisi · Geçici edinsel yenidoğan miyasteni · Geçici yenidoğan otoimmün miyastenia gravis |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | P94.0 | E | specific | validated |
| ICD-11 | KB08.0 | E | specific | validated |
| MONDO | 0018326 | E | validated | |
| UMLS | C0495465 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:589Myasthenia gravis
rare neurological diseases; rare ophthalmic disorders - ORPHA:398091Secondary neonatal autoimmune disease
rare systemic and rheumatological diseases; rare systemic or rheumatologic diseases of childhood
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/391504
- This record as JSON: /data/d/391504.json