{"orpha":391504,"name":"Transient neonatal myasthenia gravis","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["NMG","Neonatal myasthenia gravis","Transient neonatal acquired myasthenia","Transient neonatal autoimmune myasthenia gravis"],"definition":"Transient neonatal myasthenia gravis (MG) is a rare form of MG occurring in neonates born to mothers who have the disorder or specific circulating autoantibodies.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-391504/","orphanet_url":"https://www.orpha.net/en/disease/detail/391504","names":{"fr":{"name":"Myasthénie auto-immune transitoire du nouveau-né","synonyms":["Myasthenia gravis transitoire du nouveau-né","Myasthénie acquise transitoire du nouveau-né","Myasthénie auto-immune du nouveau-né","NMG"],"definition":"Forme rare de MG (pour myasthenia gravis en anglais) survenant chez les nouveau-nés de mères atteintes de la maladie ou présentant des auto-anticorps circulants spécifiques."},"de":{"name":"Transiente neonatale Myasthenia gravis","synonyms":["Myasthenie, erworbene neonatale transiente","NMG","Neonatale Myasthenia gravis","Neonatale autoimmune Myasthenia gravis, transiente Form"],"definition":"Die transiente neonatale Myasthenia gravis (MG) ist eine seltene Form der MG (siehe diesen Begriff), die bei Neugeborenen von Müttern mit Myasthenia gravis auftritt und durch spezifische zirkulierende Autoantikörper der Mutter ausgelöst wird."},"es":{"name":"Miastenia grave neonatal transitoria","synonyms":["Miastenia grave autoinmune neonatal transitoria","Miastenia grave neonatal","Miastenia neonatal transitoria adquirida","NMG"],"definition":"La miastenia gravis neonatal transitoria (MG) es una forma poco frecuente de MG que se presenta en recién nacidos de madres que tienen el trastorno o autoanticuerpos circulantes específicos."},"it":{"name":"Miastenia gravis neonatale transitoria","synonyms":["Miastenia acquisita neonatale transitoria","Miastenia grave autoimmune neonatale transitoria","Miastenia gravis neonatale","NMG"]},"nl":{"name":"Voorbijgaande neonatale myasthenia gravis","synonyms":["NMG","Neonatale myasthenia gravis","Voorbijgaande neonatale auto-immune myasthenia gravis","Voorbijgaande neonatale verworven myasthenie"],"definition":"Voorbijgaande neonatale myasthenia gravis (MG) is een zeldzame vorm van MG (zie deze term) die voorkomt in pasgeborenen waarvan de moeder de ziekte of specifieke circulerende auto-antilichamen heeft."},"pt":{"name":"Miastenia gravis neonatal transitória"},"pl":{"name":"Miastenia przejściowa noworodków","synonyms":["Autoimmunologiczna miastenia przejściowa noworodków","Miastenia noworodkowa","Nabyta miastenia przejściowa noworodków","NMG"]},"cs":{"name":"Tranzientní neonatální myasthenia gravis","synonyms":["NMG","Neonatální myasthenia gravis","Tranzientní neonatální získaná myastenie","Tranzientní neonatální autoimunitní myasthenia gravis"]},"uk":{"name":"Транзиторна неонатальна miastenia gravis","synonyms":["Неонатальна міастенія","NMG","Транзиторна неонатальна набута міастенія","Транзиторна неонатальна аутоімунна міастенія"],"definition":"Transient neonatal myasthenia gravis (MG) is a rare form of MG (see this term) occurring in neonates born to mothers who have the disorder or specific circulating autoantibodies."},"zh":{"name":"新生儿短暂性重症肌无力","synonyms":["新生儿获得性自身免疫性重症肌无力"],"definition":"一过性新生儿重症肌无力(MG)是一种罕见的MG(见此术语)，本病发生在患有这种疾病或特定循环自身抗体的母亲所生的新生儿中。"},"tr":{"name":"Geçici yenidoğan myastenia gravis","synonyms":["NMG","Yenidoğan miyastenia gravisi","Geçici edinsel yenidoğan miyasteni","Geçici yenidoğan otoimmün miyastenia gravis"]}},"xrefs":[{"source":"ICD-10","code":"P94.0","qualifier":"E","icd_relation":"specific","validated":true},{"source":"ICD-11","code":"KB08.0","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"2096990223"},{"source":"MONDO","code":"0018326","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0495465","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":589,"name":"Myasthenia gravis","classifications":[181,189]},{"orpha":398091,"name":"Secondary neonatal autoimmune disease","classifications":[196,231]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Antenatal","Neonatal"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}