ORPHA:364013
Immune hydrops fetalis
Synonyms: IHF · Immune HF · Immune fetal edema · Immune fetal hydrops
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- Antenatal, Neonatal
- Status
- active
Immune hydrops fetalis (IHF), a form of HF, describes the excessive accumulation of fetal fluid within the fetal extravascular compartments and body cavities due to maternal rhesus (Rh) incompatibility.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Immune hydrops fetalis | IHF · Immune HF · Immune fetal edema · Immune fetal hydrops |
| fr | Anasarque foetoplacentaire immunologique | IHF · Anasarque foetale immunologique · HF immunologique · Hydrops fetalis immunologique · Hydrops foetoplacentaire immunologique |
| de | Hydrops fetalis, immunologischer | IHF · Immunologischer fetaler Hydrops · Immunologisches fetales Ödem |
| es | Hidropesía fetal inmunológica | Edema fetal inmunológico · HF inmunológico · Hidrops fetal inmunológico |
| it | Idrope fetale immune | Edema fetale immune · HF immune · IHF · Idropisia fetale immune |
| nl | Immune hydrops foetalis | IHF · Immune HF · Immune foetale hydrops · Immuun foetaal oedeem |
| pt | Hidropsia fetal imune | |
| pl | Immunologiczny obrzęk płodu | IHF · Immunologiczny HF |
| cs | Imunitní hydrops fetalis | IHF · Imunitní HF · Imunitní fetální edém · Imunitní fetální hydrops |
| uk | Імунна водянка плода | НВП · Імунний набряк плода · Імунна водянка плода · Імунна ВП |
| zh | 免疫性胎儿水肿 | 免疫性胎儿水肿 |
| tr | İmmün hidrops fetalis | IHF · İmmun HF · İmmun fetal ödem · İmmun fetal hidrops |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | P56.0 | E | specific | validated |
| ICD-11 | KA85.0 | E | specific | validated |
| MONDO | 0018221 | E | validated | |
| UMLS | C0455990 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:1041Hydrops fetalis
rare developmental anomalies during embryogenesis
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
| Prevalence at birth | 1-5 / 10 000 | 33.3 / 100 000 | United Kingdom | Value and class | Validated | 19334091[PMID]_[EXPERT] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/364013
- This record as JSON: /data/d/364013.json