{"orpha":364013,"name":"Immune hydrops fetalis","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["IHF","Immune HF","Immune fetal edema","Immune fetal hydrops"],"definition":"Immune hydrops fetalis (IHF), a form of HF, describes the excessive accumulation of fetal fluid within the fetal extravascular compartments and body cavities due to maternal rhesus (Rh) incompatibility.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-364013/","orphanet_url":"https://www.orpha.net/en/disease/detail/364013","names":{"fr":{"name":"Anasarque foetoplacentaire immunologique","synonyms":["IHF","Anasarque foetale immunologique","HF immunologique","Hydrops fetalis immunologique","Hydrops foetoplacentaire immunologique"],"definition":"L'anasarque foeto-placentaire immunologique (IHF), l'une des formes de l'anasarque foeto-placentaire (HF), est définie par une accumulation chez le foetus de liquide amniotique dans le compartiment extravasculaire et les cavités, causée par une incompatibilité Rhésus (Rh) foeto-maternelle."},"de":{"name":"Hydrops fetalis, immunologischer","synonyms":["IHF","Immunologischer fetaler Hydrops","Immunologisches fetales Ödem"],"definition":"Als Immunologischer Hydrops fetalis (IHF) wird eine Form des HF (siehe dort) mit exzessiver Ansammlung von fetaler Flüssigkeit in den Geweben und Körperhöhlen des Feten bezeichnet, die durch mütterliche Rhesus (Rh)-Inkompatibilität verursacht ist."},"es":{"name":"Hidropesía fetal inmunológica","synonyms":["Edema fetal inmunológico","HF inmunológico","Hidrops fetal inmunológico"],"definition":"La hidropesía fetal inmunitaria (HFI), una forma de HF (ver este término) describe la excesiva acumulación de líquido fetal en los compartimentos fetales extravasculares y en las cavidades corporales a causa de la incompatibilidad con el factor rhesus (Rh) materno."},"it":{"name":"Idrope fetale immune","synonyms":["Edema fetale immune","HF immune","IHF","Idropisia fetale immune"],"definition":"L'idrope fetale immune (IHF), una forma di HF (si veda questo termine), definisce l'accumulo di liquidi nei compartimenti extravascolari e nelle cavità del corpo del feto, a causa di incompatibilità con il fattore Rhesus (Rh) materno."},"nl":{"name":"Immune hydrops foetalis","synonyms":["IHF","Immune HF","Immune foetale hydrops","Immuun foetaal oedeem"],"definition":"Immune hydrops foetalis (IHF), een vorm van HF (zie deze term), beschrijft de overmatige accumulatie van foetale vloeistof in de foetale extravasculaire compartimenten en lichaamsholten als gevolg van maternale rhesus (Rh)-incompatibiliteit."},"pt":{"name":"Hidropsia fetal imune"},"pl":{"name":"Immunologiczny obrzęk płodu","synonyms":["IHF","Immunologiczny HF"]},"cs":{"name":"Imunitní hydrops fetalis","synonyms":["IHF","Imunitní HF","Imunitní fetální edém","Imunitní fetální hydrops"]},"uk":{"name":"Імунна водянка плода","synonyms":["НВП","Імунний набряк плода","Імунна водянка плода","Імунна ВП"],"definition":"Immune hydrops fetalis (IHF), a form of HF, describes the excessive accumulation of fetal fluid within the fetal extravascular compartments and body cavities due to maternal rhesus (Rh) incompatibility."},"zh":{"name":"免疫性胎儿水肿","synonyms":["免疫性胎儿水肿"],"definition":"免疫性胎儿水肿(IHF)是胎儿水肿的一种，描述了由于母体Rh血型不合，胎儿体液在胎儿血管外室和体腔内过度积聚。"},"tr":{"name":"İmmün hidrops fetalis","synonyms":["IHF","İmmun HF","İmmun fetal ödem","İmmun fetal hidrops"]}},"xrefs":[{"source":"ICD-10","code":"P56.0","qualifier":"E","icd_relation":"specific","validated":true},{"source":"ICD-11","code":"KA85.0","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1589938690"},{"source":"MONDO","code":"0018221","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0455990","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93890,"name":"Rare developmental defect during embryogenesis"},"parents":[{"orpha":1041,"name":"Hydrops fetalis","classifications":[147]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Antenatal","Neonatal"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"},{"type":"Prevalence at birth","qualification":"Value and class","class":"1-5 / 10 000","value":33.3,"area":"United Kingdom","status":"Validated","source":"19334091[PMID]_[EXPERT]"}],"phenotypes":null}