raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:363478

Paratesticular adenocarcinoma

Synonyms: Adenocarcinoma of the paratestis

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

A rare, locally invasive or malignant, urogenital tumor characterized by a gland-forming epithelial neoplasm arising from paratesticular structures, typically manifesting with a palpable scrotal mass, with or without hydrocele, and/or testicular pain.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enParatesticular adenocarcinomaAdenocarcinoma of the paratestis
frAdénocarcinome paratesticulaireAdénocarcinome des structures paratesticulaires
deAdenokarzinom, paratestikuläresAdenokarzinom des paratestikulären Gewebes
esAdenocarcinoma paratesticularAdenocarcinoma del paratestículo
itAdenocarcinoma paratesticolareAdenocarcinoma paratesticolare
nlParatesticulair adenocarcinoomAdenocarcinoom van de paratestis
ptAdenocarcinoma paratesticularAdenocarcinoma paratestis
plGruczolakorak okołojądrowy= en
csParatestikulární adenokarcinomAdenokarcinom paratestikulární
ukПаратестикулярна аденокарциномаАденокарцинома паратестису
zh附睾腺癌附睾腺癌
trParatestiküler adenokarsinomParatestisin adenokarsinomu

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C63.0BTNTattributedvalidated
ICD-10C63.1BTNTattributedvalidated
ICD-10C63.2BTNTattributedvalidated
ICD-10C63.7BTNTattributedvalidated
ICD-10C63.8BTNTattributedvalidated
MONDO0018192Evalidated
UMLSC5190800Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

14 records
TypeClassValueAreaQualificationValidationSource
Lifetime Prevalence<1 / 1 000 0000.01 / 100 000EuropeValue and classValidated22033323[PMID]_RARECARE surveillance of rare cancers in Europe[OTHER]
Point prevalence<1 / 1 000 000—EuropeClass onlyNot yet validatedORPHANET
Annual incidence<1 / 1 000 000—EuropeClass onlyValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.004 / 100 000BelgiumValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000CroatiaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.001 / 100 000Czech RepublicValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.001 / 100 000GermanyValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000IrelandValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.001 / 100 000ItalyValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.005 / 100 000LatviaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000SpainValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.001 / 100 000NetherlandsValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.002 / 100 000United KingdomValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000AustriaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card