{"orpha":363478,"name":"Paratesticular adenocarcinoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Adenocarcinoma of the paratestis"],"definition":"A rare, locally invasive or malignant, urogenital tumor characterized by a gland-forming epithelial neoplasm arising from paratesticular structures, typically manifesting with a palpable scrotal mass, with or without hydrocele, and/or testicular pain.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-363478/","orphanet_url":"https://www.orpha.net/en/disease/detail/363478","names":{"fr":{"name":"Adénocarcinome paratesticulaire","synonyms":["Adénocarcinome des structures paratesticulaires"],"definition":"Tumeur urogénitale rare, localement invasive ou maligne, caractérisée par un néoplasme épithélial apparaissant sous la forme d'une glande et prenant naissance dans les structures paratesticulaires, qui se manifeste généralement par une masse scrotale palpable, avec ou sans hydrocèle, et/ou par une douleur testiculaire."},"de":{"name":"Adenokarzinom, paratestikuläres","synonyms":["Adenokarzinom des paratestikulären Gewebes"]},"es":{"name":"Adenocarcinoma paratesticular","synonyms":["Adenocarcinoma del paratestículo"],"definition":"Es un tumor urogenital poco frecuente, localmente invasivo o maligno, caracterizado por una neoplasia epitelial formadora de glándulas. Este tumor surge de las estructuras paratesticulares y se manifiesta típicamente como una masa escrotal palpable, con o sin hidrocele, y/o dolor testicular."},"it":{"name":"Adenocarcinoma paratesticolare","synonyms":["Adenocarcinoma paratesticolare"],"definition":"È un tumore urogenitale maligno raro localmente invasivo, consistente in una neoplasia epiteliale con formazione ghiandolare che origina dalle strutture paratesticolari. Di solito si manifesta come massa palpabile localizzata nello scroto, con o senza idrocele, e/o dolore testicolare."},"nl":{"name":"Paratesticulair adenocarcinoom","synonyms":["Adenocarcinoom van de paratestis"],"definition":"Een zeldzame, lokaal invasieve of maligne, urogenitale tumor die gekarakteriseerd wordt door een kliervormend, epitheliaal neoplasma dat ontstaat uit paratesticulaire structuren en zich doorgaans manifesteert met een tastbare scrotale massa, met of zonder hydrocèle, en/of testiculaire pijn."},"pt":{"name":"Adenocarcinoma paratesticular","synonyms":["Adenocarcinoma paratestis"]},"pl":{"name":"Gruczolakorak okołojądrowy","synonyms":["Adenocarcinoma of the paratestis"]},"cs":{"name":"Paratestikulární adenokarcinom","synonyms":["Adenokarcinom paratestikulární"]},"uk":{"name":"Паратестикулярна аденокарцинома","synonyms":["Аденокарцинома паратестису"],"definition":"A rare, locally invasive or malignant, urogenital tumor characterized by a gland-forming epithelial neoplasm arising from paratesticular structures, typically manifesting with a palpable scrotal mass, with or without hydrocele, and/or testicular pain."},"zh":{"name":"附睾腺癌","synonyms":["附睾腺癌"],"definition":"本病是一种罕见的、局部侵袭性或恶性泌尿生殖系统肿瘤，其特征为源于睾丸旁结构的腺体形成性上皮肿瘤，通常表现为可触及的阴囊肿块，有或无鞘膜积液和/或睾丸疼痛。"},"tr":{"name":"Paratestiküler adenokarsinom","synonyms":["Paratestisin adenokarsinomu"]}},"xrefs":[{"source":"ICD-10","code":"C63.0","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C63.1","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C63.2","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C63.7","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C63.8","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0018192","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5190800","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":363472,"name":"Tumor of testis and paratestis","classifications":[185,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Lifetime Prevalence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.01,"area":"Europe","status":"Validated","source":"22033323[PMID]_RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Europe","status":"Not yet validated","source":"ORPHANET"},{"type":"Annual incidence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.004,"area":"Belgium","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.003,"area":"Croatia","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.001,"area":"Czech Republic","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.001,"area":"Germany","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.003,"area":"Ireland","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.001,"area":"Italy","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.005,"area":"Latvia","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.003,"area":"Spain","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.001,"area":"Netherlands","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.002,"area":"United Kingdom","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.003,"area":"Austria","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"}],"phenotypes":null}