ORPHA:3282
Multifocal atrial tachycardia
Synonyms: Chaotic atrial tachycardia · MAT
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Infancy, Neonatal
- Status
- active
Multifocal atrial tachycardia is a rare supraventricular arrhythmia in neonates and young infants that is characterized by multiple P waves with varying P wave morphology and is usually asymptomatic.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Multifocal atrial tachycardia | Chaotic atrial tachycardia · MAT |
| fr | Tachycardie atriale multifocale | MAT · Tachycardie atriale chaotique · Tachycardie auriculaire chaotique · Tachysystolie atriale chaotique · Tachysystolie auriculaire chaotique · Tachysystolie auriculaire multifocale chez l'enfant |
| de | Multifokale atriale Tachykardie | MAT · Vorhoftachykardie, chaotische · Vorhoftachykardie, multifokale |
| es | Taquicardia auricular multifocal | MAT · Taquicardia atrial caótica · Taquicardia atrial multifocal |
| it | Tachicardia atriale multifocale | Tachicardia atriale caotica · MAT |
| nl | Multifocale atriumtachycardie | Chaotische atriale tachycardie · MAT |
| pt | Taquicardia auricular multifocal | Taquicardia auricular caótica |
| pl | Wieloogniskowy częstoskurcz przedsionkowy | Chaotyczny częstoskurcz przedsionkowy · MAT |
| cs | Multifokální atriální tachykardie | Chaotická atriální tachykardie · MAT |
| uk | Мультифокальна передсердна тахікардія | Хаотична передсердна тахікардія · МАТ |
| zh | 多灶性房性心动过速 | 紊乱性房性心动过速 |
| tr | Multifokal atriyal taşikardi | MAT · Kaotik atriyal taşikardi |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I47.1 | NTBT | attributed | validated |
| ICD-11 | BC81.Y | NTBT | index | validated |
| MONDO | 0017988 | E | validated | |
| UMLS | C0221158 | E | validated | |
| GARD | 1235 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:218439Non-genetic cardiac rhythm disease
rare cardiac diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Prevalence at birth | 1-9 / 1 000 000 | 0.67 / 100 000 | Worldwide | Value and class | Validated | ORPHANET |
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
25 annotations · validated 2023-03-31| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Obligate (100%) | ||
| HP:0031593 | Abnormal PR interval | |
| HP:6001087 | Irregular P-P interval | |
| HP:6001086 | Irregular RR interval | |
| HP:0001649 | Tachycardia | |
| Frequent (79-30%) | ||
| HP:0005110 | Atrial fibrillation | |
| HP:0004749 | Atrial flutter | |
| HP:0034376 | Atrioventricular valve regurgitation | |
| HP:6000264 | Fetal tachycardia | |
| Occasional (29-5%) | ||
| HP:0005162 | Abnormal left ventricular function | |
| HP:0001631 | Atrial septal defect | |
| HP:0011717 | Atrioventricular reentrant tachycardia | |
| HP:0002094 | Dyspnea | |
| HP:0004758 | Effort-induced polymorphic ventricular tachycardia | |
| HP:0008872 | Feeding difficulties in infancy | |
| HP:0001639 | Hypertrophic cardiomyopathy | |
| HP:0002615 | Hypotension | |
| HP:4000141 | Left ventricular dilatation | |
| HP:0001642 | Pulmonic stenosis | |
| HP:0002789 | Tachypnea | |
| HP:0001629 | Ventricular septal defect | |
| Very rare (<4-1%) | ||
| HP:0000028 | Cryptorchidism | |
| HP:0000821 | Hypothyroidism | |
| HP:0001254 | Lethargy | |
| HP:0006671 | Paroxysmal atrial tachycardia | |
| HP:0001279 | Syncope | |
Run the differential on the 4 obligate / very frequent terms
Annotation source: 29441747[PMID]_35813391[PMID]
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/3282
- This record as JSON: /data/d/3282.json