{"orpha":3282,"name":"Multifocal atrial tachycardia","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Chaotic atrial tachycardia","MAT"],"definition":"Multifocal atrial tachycardia is a rare supraventricular arrhythmia in neonates and young infants that is characterized by multiple P waves with varying P wave morphology and is usually asymptomatic.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-3282/","orphanet_url":"https://www.orpha.net/en/disease/detail/3282","names":{"fr":{"name":"Tachycardie atriale multifocale","synonyms":["MAT","Tachycardie atriale chaotique","Tachycardie auriculaire chaotique","Tachysystolie atriale chaotique","Tachysystolie auriculaire chaotique","Tachysystolie auriculaire multifocale chez l'enfant"],"definition":"La tachycardie atriale multifocale (TAM) est un trouble rare du rythme supra-ventriculaire chez des nouveau-nés et des nourrissons, caractérisé par de multiples ondes P ayant une morphologie variée. Elle est généralement asymptomatique."},"de":{"name":"Multifokale atriale Tachykardie","synonyms":["MAT","Vorhoftachykardie, chaotische","Vorhoftachykardie, multifokale"],"definition":"Die Multifokale Vorhoftachykardie ist eine sehr seltene supraventrikuläre Arrhythmie des Säuglings- und frühen Kleinkindalters. Kennzeichnend sind morphologisch unterschiedliche multiple P-Wellen. In der Regel bestehen keine Symptome."},"es":{"name":"Taquicardia auricular multifocal","synonyms":["MAT","Taquicardia atrial caótica","Taquicardia atrial multifocal"],"definition":"La taquicardia auricular multifocal (TAM) es una arritmia supraventricular rara en neonatos y lactantes, que se caracteriza por múltiples ondas P con morfologías variables, y suele ser asintomática."},"it":{"name":"Tachicardia atriale multifocale","synonyms":["Tachicardia atriale caotica","MAT"],"definition":"La tachicardia atriale multifocale è un'aritmia sopraventricolare rara dei neonati e dei lattanti che si caratterizza per la presenza di onde P multiple con morfologia P variabile; di solito è asintomatica."},"nl":{"name":"Multifocale atriumtachycardie","synonyms":["Chaotische atriale tachycardie","MAT"],"definition":"Multifocale atriale tachycardie is een zeldzame supraventriculaire aritmie bij neonaten en jonge zuigelingen die wordt gekenmerkt door meerdere P-golven met verschillende P-golfmorfologie en die meestal asymptomatisch is."},"pt":{"name":"Taquicardia auricular multifocal","synonyms":["Taquicardia auricular caótica"]},"pl":{"name":"Wieloogniskowy częstoskurcz przedsionkowy","synonyms":["Chaotyczny częstoskurcz przedsionkowy","MAT"]},"cs":{"name":"Multifokální atriální tachykardie","synonyms":["Chaotická atriální tachykardie","MAT"]},"uk":{"name":"Мультифокальна передсердна тахікардія","synonyms":["Хаотична передсердна тахікардія","МАТ"],"definition":"Multifocal atrial tachycardia is a rare supraventricular arrhythmia in neonates and young infants that is characterized by multiple P waves with varying P wave morphology and is usually asymptomatic."},"zh":{"name":"多灶性房性心动过速","synonyms":["紊乱性房性心动过速"]},"tr":{"name":"Multifokal atriyal taşikardi","synonyms":["MAT","Kaotik atriyal taşikardi"]}},"xrefs":[{"source":"ICD-10","code":"I47.1","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"BC81.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"262929566"},{"source":"MONDO","code":"0017988","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0221158","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"1235","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97929,"name":"Rare cardiac disease"},"parents":[{"orpha":218439,"name":"Non-genetic cardiac rhythm disease","classifications":[146]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Infancy","Neonatal"],"prevalence":[{"type":"Prevalence at birth","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.67,"area":"Worldwide","status":"Validated","source":"ORPHANET"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":{"validation_status":"y","online":"y","validation_date":"2023-03-31","source":"29441747[PMID]_35813391[PMID]","terms":[{"hpo":"HP:0031593","label":"Abnormal PR interval","frequency":"Obligate (100%)","criteria":null},{"hpo":"HP:6001087","label":"Irregular P-P interval","frequency":"Obligate (100%)","criteria":null},{"hpo":"HP:6001086","label":"Irregular RR interval","frequency":"Obligate (100%)","criteria":null},{"hpo":"HP:0001649","label":"Tachycardia","frequency":"Obligate (100%)","criteria":null},{"hpo":"HP:0005110","label":"Atrial fibrillation","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0004749","label":"Atrial flutter","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0034376","label":"Atrioventricular valve regurgitation","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:6000264","label":"Fetal tachycardia","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0005162","label":"Abnormal left ventricular function","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0001631","label":"Atrial septal defect","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0011717","label":"Atrioventricular reentrant tachycardia","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0002094","label":"Dyspnea","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0004758","label":"Effort-induced polymorphic ventricular tachycardia","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0008872","label":"Feeding difficulties in infancy","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0001639","label":"Hypertrophic cardiomyopathy","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0002615","label":"Hypotension","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:4000141","label":"Left ventricular dilatation","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0001642","label":"Pulmonic stenosis","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0002789","label":"Tachypnea","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0001629","label":"Ventricular septal defect","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0000028","label":"Cryptorchidism","frequency":"Very rare (<4-1%)","criteria":null},{"hpo":"HP:0000821","label":"Hypothyroidism","frequency":"Very rare (<4-1%)","criteria":null},{"hpo":"HP:0001254","label":"Lethargy","frequency":"Very rare (<4-1%)","criteria":null},{"hpo":"HP:0006671","label":"Paroxysmal atrial tachycardia","frequency":"Very rare (<4-1%)","criteria":null},{"hpo":"HP:0001279","label":"Syncope","frequency":"Very rare (<4-1%)","criteria":null}]}}