ORPHA:314466
Atypical Meigs syndrome
Synonyms: Atypical Demons-Meigs syndrome · Incomplete Meigs syndrome
- Type
- Clinical syndrome
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A rare benign ovarian tumor characterized by a benign pelvic mass associated with right-sided pleural effusion, but without ascites. The pleural effusion resolves after resection of the tumor.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Atypical Meigs syndrome | Atypical Demons-Meigs syndrome · Incomplete Meigs syndrome |
| fr | Syndrome de Meigs atypique | Syndrome de Demons-Meigs atypique |
| de | Meigs-Syndrom, atypisches | Demons-Meigs-Syndrom, atypisches · Meigs-Syndrom, inkomplettes |
| es | Síndrome de Meigs atípico | Síndrome de Demons-Meigs atípico · Síndrome de Meigs incompleto |
| it | Sindrome di Meigs atipica | Sindrome di Demons-Meigs atipica |
| nl | Atypisch syndroom van Meigs | Atypisch syndroom van Demons-Meigs · Onvolledig syndroom van Meigs |
| pt | Síndrome de Meigs atípico | Síndrome de Demons-Meigs atípico |
| pl | Atypowy zespół Meigsa | Atypowy zespół Demonsa i Meigsa |
| cs | Atypický Meigsův syndrom | Atypický Demonsův-Meigsův syndrom · Atypický Demons-Meigsův syndrom |
| uk | Атиповий синдром Мейгса | Атиповий синдром Демонса-Мейгса · Неповний синдром Мейгса |
| zh | 非典型Meigs综合征 | 非典型Demons-Meigs综合征 |
| tr | Atipik Meigs sendromu | Eksik Meigs sendromu · Atipik Demons-Meigs sendromu |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D27 | NTBT | attributed | validated |
| ICD-11 | 2F32.2 | NTBT | attributed | validated |
| MONDO | 0017801 | E | validated | |
| UMLS | C5190605 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:97293Rare benign ovarian tumor
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Cases/families | 9 cases | Worldwide | Case(s) | Validated | 7112481[PMID]_9336761[PMID]_12632574[PMID]_12087934[PMID]_15739106[PMID] | |
| Point prevalence | <1 / 1 000 000 | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/314466
- This record as JSON: /data/d/314466.json