{"orpha":314466,"name":"Atypical Meigs syndrome","type":"Clinical syndrome","group":"Disorder","status":"active","flags":[],"synonyms":["Atypical Demons-Meigs syndrome","Incomplete Meigs syndrome"],"definition":"A rare benign ovarian tumor characterized by a benign pelvic mass associated with right-sided pleural effusion, but without ascites. The pleural effusion resolves after resection of the tumor.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-314466/","orphanet_url":"https://www.orpha.net/en/disease/detail/314466","names":{"fr":{"name":"Syndrome de Meigs atypique","synonyms":["Syndrome de Demons-Meigs atypique"],"definition":"Tumeur bénigne rare de l'ovaire caractérisée par une masse pelvienne bénigne associée à un épanchement pleural droit, en l'absence d'ascites. L'épanchement pleural se résorbe après résection de la tumeur."},"de":{"name":"Meigs-Syndrom, atypisches","synonyms":["Demons-Meigs-Syndrom, atypisches","Meigs-Syndrom, inkomplettes"]},"es":{"name":"Síndrome de Meigs atípico","synonyms":["Síndrome de Demons-Meigs atípico","Síndrome de Meigs incompleto"],"definition":"Es un tumor de ovario benigno poco frecuente caracterizado por una masa pélvica benigna asociada a derrame pleural derecho, pero sin ascitis. El derrame pleural se resuelve después de la resección tumoral."},"it":{"name":"Sindrome di Meigs atipica","synonyms":["Sindrome di Demons-Meigs atipica"],"definition":"La sindrome di Meigs atipica è un tumore benigno raro dell'ovaio, caratterizzato da una massa pelvica benigna associata a versamento pleurico destro, in assenza di asciti. Il versamento pleurico si risolve con la resezione del tumore."},"nl":{"name":"Atypisch syndroom van Meigs","synonyms":["Atypisch syndroom van Demons-Meigs","Onvolledig syndroom van Meigs"],"definition":"Een zeldzame, goedaardige ovariële tumor, gekarakteriseerd door een goedaardige pelviene massa geassocieerd met pleura-effusie aan de rechter zijde, maar zonder ascites. De pleura-effusie verdwijnt na resectie van de tumor."},"pt":{"name":"Síndrome de Meigs atípico","synonyms":["Síndrome de Demons-Meigs atípico"]},"pl":{"name":"Atypowy zespół Meigsa","synonyms":["Atypowy zespół Demonsa i Meigsa"]},"cs":{"name":"Atypický Meigsův syndrom","synonyms":["Atypický Demonsův-Meigsův syndrom","Atypický Demons-Meigsův syndrom"]},"uk":{"name":"Атиповий синдром Мейгса","synonyms":["Атиповий синдром Демонса-Мейгса","Неповний синдром Мейгса"],"definition":"A rare benign ovarian tumor characterized by a benign pelvic mass associated with right-sided pleural effusion, but without ascites. The pleural effusion resolves after resection of the tumor."},"zh":{"name":"非典型Meigs综合征","synonyms":["非典型Demons-Meigs综合征"],"definition":"一种罕见的良性卵巢肿瘤，其特征是良性盆腔肿块伴右侧胸腔积液，但无腹水。胸腔积液在肿瘤切除后消失。"},"tr":{"name":"Atipik Meigs sendromu","synonyms":["Eksik Meigs sendromu","Atipik Demons-Meigs sendromu"]}},"xrefs":[{"source":"ICD-10","code":"D27","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2F32.2","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0017801","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5190605","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":97293,"name":"Rare benign ovarian tumor","classifications":[202,205]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":9.0,"area":"Worldwide","status":"Validated","source":"7112481[PMID]_9336761[PMID]_12632574[PMID]_12087934[PMID]_15739106[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}