Pseudo-Meigs syndrome
Synonyms: Pseudo-Demons-Meigs syndrome
- Type
- Clinical syndrome
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A rare neoplastic disease characterized by the presence of a benign or malignant, pelvic or abdominal tumor (other than ovarian fibroma or fibroma-like and localized outside of the ovaries, fallopian tubes, and broad ligaments) associated with hydrothorax and ascites that resolve after tumor resection. Patients usually present with dyspnea, pelvic mass with or without a tender, distended abdomen and/or weight loss.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Pseudo-Meigs syndrome | Pseudo-Demons-Meigs syndrome |
| fr | Syndrome pseudo-Meigs | Syndrome pseudo-Demons-Meigs |
| de | Pseudo-Meigs-Syndrom | Pseudo-Demons-Meigs-Syndrom |
| es | Síndrome de pseudo-Meigs | Síndrome de pseudo-Demons-Meigs |
| it | Sindrome pseudo-Meigs | Sindrome pseudo-Demons-Meigs |
| nl | Pseudo-Meigssyndroom | Pseudo-Demons-Meigssyndroom |
| pt | Síndrome pseudo-Meigs | Síndrome pseudo-Demons-Meigs |
| pl | Rzekomy zespół Meigsa | Rzekomy zespół Demonsa i Meigsa |
| cs | Pseudo-Meigsův syndrom | Pseudo-Demonsův-Meigsův syndrom · Pseudo-Demons-Meigsův syndrom |
| uk | Синдром псевдо-Мейгса | Синдром псевдодемонів-Мейгса |
| zh | 假性Meigs综合征 | Pseudo-Demons-Meigs综合征 |
| tr | Sözde Meigs sendromu | Pseudo-Demons-Meigs sendromu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D39.1 | NTBT | attributed | validated |
| ICD-11 | 2F32.2 | NTBT | attributed | validated |
| MONDO | 0017800 | E | validated | |
| UMLS | C5190824 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:97293Rare benign ovarian tumor
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/314459
- This record as JSON: /data/d/314459.json