{"orpha":314459,"name":"Pseudo-Meigs syndrome","type":"Clinical syndrome","group":"Disorder","status":"active","flags":[],"synonyms":["Pseudo-Demons-Meigs syndrome"],"definition":"A rare neoplastic disease characterized by the presence of a benign or malignant, pelvic or abdominal tumor (other than ovarian fibroma or fibroma-like and localized outside of the ovaries, fallopian tubes, and broad ligaments) associated with hydrothorax and ascites that resolve after tumor resection. Patients usually present with dyspnea, pelvic mass with or without a tender, distended abdomen and/or weight loss.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-314459/","orphanet_url":"https://www.orpha.net/en/disease/detail/314459","names":{"fr":{"name":"Syndrome pseudo-Meigs","synonyms":["Syndrome pseudo-Demons-Meigs"],"definition":"Maladie néoplasique rare caractérisée par la présence d'une tumeur pelvienne ou abdominale bénigne ou maligne (autre qu'un fibrome ovarien ou de type fibrome, localisée en dehors des ovaires, des trompes de Fallope et des ligaments larges) associée à un hydrothorax et à une ascite qui se résorbent après la résection de la tumeur. Les patientes présentent généralement une dyspnée, une masse pelvienne avec ou sans sensibilité ou distension abdominale et/ou une perte de poids."},"de":{"name":"Pseudo-Meigs-Syndrom","synonyms":["Pseudo-Demons-Meigs-Syndrom"]},"es":{"name":"Síndrome de pseudo-Meigs","synonyms":["Síndrome de pseudo-Demons-Meigs"],"definition":"Es una enfermedad neoplásica poco frecuente caracterizada por la presencia de un tumor pélvico o abdominal, benigno o maligno (distinto al fibroma ovárico o de tipo fibroma ovárico y localizado fuera de los ovarios, de las trompas de Falopio y de los ligamentos anchos) asociado a hidrotórax y ascitis que remiten con la resección tumoral. Por lo general, las pacientes presentan disnea, masa pélvica con o sin abdomen sensible al tacto, distendido y/o pérdida de peso."},"it":{"name":"Sindrome pseudo-Meigs","synonyms":["Sindrome pseudo-Demons-Meigs"],"definition":"La sindrome pseudo-Meigs è una neoplasia rara, consistente in un tumore pelvico o addominale (diverso dal fibroma o dal simil-fibroma ovarico, localizzato al di fuori dell'ovaio, delle tube di Falloppio e dei ligamenti larghi) benigno o maligno, associato a idrotorace e ascite, che si risolvono dopo la resezione del tumore. Di solito le pazienti presentano dispnea, una massa pelvica con o senza ipersensibilità e distensione dell'addome e/o perdita di peso."},"nl":{"name":"Pseudo-Meigssyndroom","synonyms":["Pseudo-Demons-Meigssyndroom"],"definition":"Pseudo-Meigssyndroom is een zeldzame, neoplastische ziekte die gekarakteriseerd wordt door de aanwezigheid van een goed- of kwaadaardige, pelviene of abdominale tumor (verschillend van ovarieel fibroom of fibroom-achtig en gesitueerd buiten de ovaria, eileiders, en brede ligamenten), geassocieerd met hydrothorax en ascites die verdwijnen na resectie van de tumor. Patiënten vertonen meestal dyspneu, pelviene massa met of zonder een gevoelige en opgezette buik, en/of gewichtsverlies."},"pt":{"name":"Síndrome pseudo-Meigs","synonyms":["Síndrome pseudo-Demons-Meigs"]},"pl":{"name":"Rzekomy zespół Meigsa","synonyms":["Rzekomy zespół Demonsa i Meigsa"]},"cs":{"name":"Pseudo-Meigsův syndrom","synonyms":["Pseudo-Demonsův-Meigsův syndrom","Pseudo-Demons-Meigsův syndrom"]},"uk":{"name":"Синдром псевдо-Мейгса","synonyms":["Синдром псевдодемонів-Мейгса"],"definition":"A rare neoplastic disease characterized by the presence of a benign or malignant, pelvic or abdominal tumor (other than ovarian fibroma or fibroma-like and localized outside of the ovaries, fallopian tubes, and broad ligaments) associated with hydrothorax and ascites that resolve after tumor resection. Patients usually present with dyspnea, pelvic mass with or without a tender, distended abdomen and/or weight loss."},"zh":{"name":"假性Meigs综合征","synonyms":["Pseudo-Demons-Meigs综合征"],"definition":"假性梅格斯综合征是一种罕见的肿瘤性疾病，其特征是良性或恶性盆腔或腹部肿瘤（卵巢纤维瘤或纤维瘤样肿瘤除外，位于卵巢、输卵管和广泛韧带之外），伴有胸水和腹水，肿瘤切除后可消退。患者通常表现为呼吸困难、盆腔肿块伴或不伴腹部压痛、腹胀和/或体重减轻。"},"tr":{"name":"Sözde Meigs sendromu","synonyms":["Pseudo-Demons-Meigs sendromu"]}},"xrefs":[{"source":"ICD-10","code":"D39.1","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2F32.2","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0017800","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5190824","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":97293,"name":"Rare benign ovarian tumor","classifications":[202,205]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}