raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:314451

Meigs syndrome

Synonyms: Demons-Meigs syndrome

Type
Clinical syndrome
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

Meigs syndrome is a rare neoplastic disease characterized by the clinical triad of benign ovarian tumor (typically, ovarian fibroma or fibroma-like tumor), hydrothorax and ascites, which resolve after tumor resection. Patients usually present with dyspnea, pelvic mass with or without a tender, distended abdomen and/or weight loss.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enMeigs syndromeDemons-Meigs syndrome
frSyndrome de MeigsSyndrome de Demons-Meigs
deMeigs-SyndromDemons-Meigs-Syndrom
esSíndrome de MeigsSíndrome de Demons-Meigs
itSindrome di MeigsSindrome di Demons-Meigs
nlSyndroom van MeigsSyndroom van Demons-Meigs
ptSíndrome de MeigsSíndrome de Demons-Meigs
plZespół MeigsaZespół Demonsa i Meigsa
csMeigsův syndromDemonsův-Meigsův syndrom · Demons-Meigsův syndrom
ukСиндром МейгсаСиндром Демонса-Мейгса
zhMeigs综合征Demons-Meigs综合征
trMeigs sendromuDemons-Meigs sendromu

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10D27NTBTattributedvalidated
ICD-112F32.2Especificvalidated
MONDO0017799Evalidated
MeSHD008539Evalidated
UMLSC0025184Evalidated
MedDRA10027139Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card