{"orpha":314451,"name":"Meigs syndrome","type":"Clinical syndrome","group":"Disorder","status":"active","flags":[],"synonyms":["Demons-Meigs syndrome"],"definition":"Meigs syndrome is a rare neoplastic disease characterized by the clinical triad of benign ovarian tumor (typically, ovarian fibroma or fibroma-like tumor), hydrothorax and ascites, which resolve after tumor resection. Patients usually present with dyspnea, pelvic mass with or without a tender, distended abdomen and/or weight loss.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-314451/","orphanet_url":"https://www.orpha.net/en/disease/detail/314451","names":{"fr":{"name":"Syndrome de Meigs","synonyms":["Syndrome de Demons-Meigs"],"definition":"Maladie néoplasique rare caractérisée par la triade clinique associant tumeur ovarienne bénigne (typiquement, un fibrome ovarien ou une tumeur de type fibrome), hydrothorax et ascite, qui disparaissent après la résection de la tumeur. Les patients présentent généralement une dyspnée, une masse pelvienne avec ou sans sensibilité et distension abdominales et/ou une perte de poids."},"de":{"name":"Meigs-Syndrom","synonyms":["Demons-Meigs-Syndrom"]},"es":{"name":"Síndrome de Meigs","synonyms":["Síndrome de Demons-Meigs"],"definition":"Es una enfermedad neoplásica poco frecuente caracterizada por una tríada clínica compuesta por tumor benigno de ovario (normalmente, fibroma ovárico o tumor tipo fibroma), hidrotórax y ascitis, que remiten tras la resección tumoral. Por lo general, las pacientes se presentan con disnea, masa pélvica con o sin abdomen sensible al tacto y distendido y/o pérdida de peso."},"it":{"name":"Sindrome di Meigs","synonyms":["Sindrome di Demons-Meigs"],"definition":"La sindrome di Meigs è una neoplasia rara caratterizzata clinicamente dalla triade: tumore ovarico benigno (di solito fibroma ovarico o tumore simil-fibroma), idrotorace ed ascite. La resezione del tumore è risolutiva. Le pazienti di solito presentano dispnea, una massa pelvica con o senza dolore e distensione dell'addome e/o perdita di peso."},"nl":{"name":"Syndroom van Meigs","synonyms":["Syndroom van Demons-Meigs"],"definition":"Syndroom van Meigs is een zeldzame, neoplastische ziekte die gekarakteriseerd wordt door de klinische triade van goedaardige ovariumtumor (doorgaans ovarieel fibroom of fibroom-achtige tumor), hydrothorax en ascites, die verdwijnen na resectie van de tumor. Patiënten vertonen meestal dyspneu, pelviene massa met of zonder een gevoelige en opgezette buik, en/of gewichtsverlies."},"pt":{"name":"Síndrome de Meigs","synonyms":["Síndrome de Demons-Meigs"]},"pl":{"name":"Zespół Meigsa","synonyms":["Zespół Demonsa i Meigsa"]},"cs":{"name":"Meigsův syndrom","synonyms":["Demonsův-Meigsův syndrom","Demons-Meigsův syndrom"]},"uk":{"name":"Синдром Мейгса","synonyms":["Синдром Демонса-Мейгса"],"definition":"Meigs syndrome is a rare neoplastic disease characterized by the clinical triad of benign ovarian tumor (typically, ovarian fibroma or fibroma-like tumor), hydrothorax and ascites, which resolve after tumor resection. Patients usually present with dyspnea, pelvic mass with or without a tender, distended abdomen and/or weight loss."},"zh":{"name":"Meigs综合征","synonyms":["Demons-Meigs综合征"],"definition":"梅格斯综合征是一种少见的肿瘤性疾病，临床表现为卵巢良性肿瘤（通常为卵巢纤维瘤或纤维瘤样肿瘤）、胸水和腹水，肿瘤切除后消退。患者通常表现为呼吸困难、盆腔肿块伴或不伴腹部压痛、腹胀和/或体重减轻。"},"tr":{"name":"Meigs sendromu","synonyms":["Demons-Meigs sendromu"]}},"xrefs":[{"source":"ICD-10","code":"D27","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2F32.2","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1050919535"},{"source":"MONDO","code":"0017799","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D008539","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0025184","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10027139","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":97293,"name":"Rare benign ovarian tumor","classifications":[202,205]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}