ORPHA:314017
Idiopathic linear interstitial keratitis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Unknown
- Age of onset
- Adult
- Status
- active
Idiopathic linear interstitial keratitis is a rare, acquired ocular disease characterized by migratory or non-migratory, horizontal, linear, stromal infiltrates that may heal spontaneously. Minimal vascularization and scarring may be observed but vision loss is not associated.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Idiopathic linear interstitial keratitis | |
| fr | Kératite interstitielle linéaire idiopathique | |
| de | Keratitis, idiopathische interstitielle lineare | |
| es | Queratitis intersticial lineal idiopática | |
| it | Cheratite interstiziale lineare idiopatica | |
| nl | Idiopathische lineaire interstitiële keratitis | |
| pt | Queratite intersticial idiopática linear | |
| pl | Idiopatyczne linearne śródmiąższowe zapalenie rogówki | |
| cs | Idiopatická lineární intersticiální keratitida | |
| uk | Ідіопатичний лінійний інтерстиціальний кератит | |
| zh | 特发性线形间质性角膜炎 | |
| tr | İdiyopatik lineer interstisyel keratit |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | H16.3 | NTBT | attributed | validated |
| ICD-11 | 9A7Y | NTBT | attributed | validated |
| MONDO | 0017789 | E | validated | |
| UMLS | C4751438 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:519290Rare inflammatory/autoimmune corneal disorder
rare ophthalmic disorders
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/314017
- This record as JSON: /data/d/314017.json