{"orpha":314017,"name":"Idiopathic linear interstitial keratitis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Idiopathic linear interstitial keratitis is a rare, acquired ocular disease characterized by migratory or non-migratory, horizontal, linear, stromal infiltrates that may heal spontaneously. Minimal vascularization and scarring may be observed but vision loss is not associated.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-314017/","orphanet_url":"https://www.orpha.net/en/disease/detail/314017","names":{"fr":{"name":"Kératite interstitielle linéaire idiopathique","definition":"Maladie oculaire rare et acquise, caractérisée par des infiltrats stromaux horizontaux et linéaires, migratoires ou pas, qui peuvent guérir spontanément. Une réduction de la vascularisation et une cicatrisation peuvent être observées, mais sans perte de vision."},"de":{"name":"Keratitis, idiopathische interstitielle lineare"},"es":{"name":"Queratitis intersticial lineal idiopática","definition":"La queratitis intersticial lineal idiopática es una enfermedad ocular adquirida y poco frecuente caracterizada por infiltrados estromales, lineales, horizontales, migratorios o no, que pueden curar espontáneamente. Se puede observar vascularización y cicatrización mínimas, sin pérdida de visión."},"it":{"name":"Cheratite interstiziale lineare idiopatica","definition":"La cheratite interstiziale lineare idiopatica è una malattia acquisita rara dell'occhio, caratterizzata da infiltrati stromali orizzontali lineari, migranti o meno, che possono guarire spontaneamente. Può associarsi ad una vascolarizzazione minima e alla formazione di cicatrici. La malattia non causa la perdita della vista."},"nl":{"name":"Idiopathische lineaire interstitiële keratitis","definition":"Idiopathische lineaire interstitiële keratitis is een zeldzame, verworven oogziekte die gekarakteriseerd wordt door migratorische of niet-migratorische, horizontale, lineaire, stromale infiltraten en die spontaan kan genezen. Minimale vascularisatie en littekenvorming kunnen waargenomen worden, maar verlies van gezichtsvermogen is niet geassocieerd."},"pt":{"name":"Queratite intersticial idiopática linear"},"pl":{"name":"Idiopatyczne linearne śródmiąższowe zapalenie rogówki","definition":"*Idiopatyczne linearne śródmiąższowe zapalenie rogówki jest rzadką, nabytą chorobą oczu, która charakteryzuje się wędrującymi (lub nie), poziomymi, liniowymi naciekami zrębu, które mogą goić się samoistnie. Można zaobserwować zmniejszone unaczynienie i bliznowacenie, jednak bez utraty wzroku."},"cs":{"name":"Idiopatická lineární intersticiální keratitida"},"uk":{"name":"Ідіопатичний лінійний інтерстиціальний кератит","definition":"Idiopathic linear interstitial keratitis is a rare, acquired ocular disease characterized by migratory or non-migratory, horizontal, linear, stromal infiltrates that may heal spontaneously. Minimal vascularization and scarring may be observed but vision loss is not associated."},"zh":{"name":"特发性线形间质性角膜炎","definition":"特发性线性间质性角膜炎是一种罕见的获得性眼病，其特征是可自行愈合的移行性或非移行性水平线性间质浸润。可以观察到微小的血管化和疤痕，但无视力下降。"},"tr":{"name":"İdiyopatik lineer interstisyel keratit"}},"xrefs":[{"source":"ICD-10","code":"H16.3","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"9A7Y","qualifier":"NTBT","icd_relation":"attributed","validated":true,"icd11_uri":"null"},{"source":"MONDO","code":"0017789","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4751438","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97966,"name":"Rare ophthalmic disorder"},"parents":[{"orpha":519290,"name":"Rare inflammatory/autoimmune corneal disorder","classifications":[189]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Unknown"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}