ORPHA:313920
Epstein-Barr virus-associated gastric carcinoma
Synonyms: EBV-associated gastric carcinoma · EBVaGC
- Type
- Disease
- Group
- Disorder
- Inheritance
- Multigenic/multifactorial
- Age of onset
- Adult, Elderly
- Status
- active
A rare form of gastric carcinoma characterized by a latent EBV infection in gastric carcinoma cells, diffuse-type histology, a proximal location (in the body and cardia of the stomach) and a relatively favorable prognosis.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Epstein-Barr virus-associated gastric carcinoma | EBV-associated gastric carcinoma · EBVaGC |
| fr | Carcinome gastrique associé au virus Epstein-Barr | Carcinome gastrique associé à l'EBV · EBVaGC |
| de | Epstein-Barr Virus-assoziiertes Magenkarzinom | EBVaGC · Magenkrebs, EBV-assoziierter |
| es | Carcinoma gástrico asociado al virus de Epstein-Barr | Carcinoma gástrico asociado a EBV · EBVaGC |
| it | Carcinoma gastrico associato al virus di Epstein-Barr | Carcinoma gastrico EBV-associato · EBVaGC |
| nl | Epstein-Barrvirus-geassocieerd gastrisch carcinoom | EBV-geassocieerd gastrisch carcinoom · EBVaGC |
| pt | Carcinoma gástrico associado a vírus Epstein-Barr | Carcinoma gástrico associado a EBV · EBVaGC |
| pl | Rak żołądka związany z wirusem Epsteina i Barra | EBVaGC · Rak żołądka związany z EBV |
| cs | Karcinom žaludku asociovaný s virem Epsteina-Barrové | EBV-asociovaný karcinom žaludku · EBVaGC · Karcinom žaludku asociovaný s virem Epstein-Barrové |
| uk | Епштейн-Барр-асоційована карцинома шлунка | EBVaGC · EBV-асоційована карцинома шлунка |
| zh | EB病毒相关性胃癌 | EBV相关性胃癌 |
| tr | Epstein-Barr virüsü -ilişkili mide karsinomu | EBVaGC · EBV-ilişkili mide karsinomu |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C16.0 | NTBT | attributed | validated |
| ICD-10 | C16.2 | NTBT | attributed | validated |
| ICD-11 | 2B72.Y | NTBT | attributed | validated |
| MONDO | 0017784 | E | validated | |
| UMLS | C4274414 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:289651Epstein-Barr Virus-associated carcinoma
rare neoplastic diseases - ORPHA:423771Rare carcinoma of stomach
rare gastroenterological diseases; rare neoplastic diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 100 000 | 1.2 / 100 000 | Worldwide | Value and class | Not yet validated | 22392024[PMID]_ORPHANET |
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/313920
- This record as JSON: /data/d/313920.json