Ramsay Hunt syndrome
Synonyms: Facial nerve palsy due to VZV · Facial nerve palsy due to herpes zoster infection · Facial nerve paralysis due to VZV
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
A rare infectious disease characterized by herpes zoster oticus associated with peripheral facial nerve palsy, often also with other cranial nerve lesions. Patients present with a painful erythematous vesicular rash in and around one ear and facial paralysis on the same side. Other frequent manifestations include hearing loss, tinnitus, vertigo, nausea, vomiting, and nystagmus.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Ramsay Hunt syndrome | Facial nerve palsy due to VZV · Facial nerve palsy due to herpes zoster infection · Facial nerve paralysis due to VZV |
| fr | Syndrome de Ramsay Hunt | Paralysie faciale liée à l'infection par le VZV · Paralysie faciale liée à l'infection par le virus varicelle zona |
| de | Ramsay-Hunt-Syndrom | Fazialislähmung durch VZV · Fazialisparese Herpes zoster-Infektion · Fazialisparese durch Varicella-Zoster-Virus |
| es | Síndrome de Ramsay Hunt | Parálisis del nervio facial por VZV · Parálisis del nervio facial por una infección por herpes zóster |
| it | Sindrome di Ramsay Hunt | Paralisi dei nervi facciali da VZV · Paralisi dei nervi facciali dovuta a infezione da herpes zoster |
| nl | Syndroom van Ramsay Hunt | Aangezichtsverlamming door VZV · Aangezichtsverlamming door herpes zoster-infectie · Verlamming van de gelaatszenuw door VZV |
| pt | Síndrome Ramsay-Hunt | Ataxia mioclónica |
| pl | Zespół Ramsaya Hunta | Półpasiec uszny · Porażenie nerwu twarzowego z powodu półpaśca · Porażenie nerwu twarzowego z powodu VZV |
| cs | Ramsay-Huntův syndrom | Obrna lícního nervu způsobená VZV · Obrna lícního nervu způsobená infekcí herpes zoster · Obrna nervus facialis způsobená VZV |
| uk | Синдром Рамзі Ханта | Параліч лицьового нерва внаслідок інфекції оперізувального герпесу · Параліч лицьового нерва внаслідок вірусного гепатиту В · Параліч лицьового нерва внаслідок VZV |
| zh | 拉姆齐·亨特综合征 | 带状疱疹感染所致面神经麻痹 |
| tr | Ramsay Hunt sendromu | VZV'ye bağlı fasiyal sinir felci · VZV'ye bağlı fasiyal sinir paraliz · Herpes zoster enfeksiyonuna bağlı fasiyal sinir felci |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | B02.2+ | NTBT | index | validated |
| ICD-10 | G53.0* | NTBT | index | validated |
| ICD-11 | 8B88.Y | NTBT | index | validated |
| MONDO | 0005769 | E | validated | |
| MONDO | 5769 | E | validated | |
| UMLS | C0017409 | E | validated | |
| GARD | 7525 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:206613Infectious disease with peripheral neuropathy
rare neurological diseases - ORPHA:163585Rare viral disease
rare infectious diseases
No children.
Codes that Orphanet moved or referred to this one:
- ORPHA:412220OBSOLETE: Ramsay Hunt syndrome type II referred to · inactive
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 100 000 | 5 / 100 000 | United States | Value and class | Validated | 23763077[PMID]_24799517[PMID] |
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/3020
- This record as JSON: /data/d/3020.json