{"orpha":3020,"name":"Ramsay Hunt syndrome","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Facial nerve palsy due to VZV","Facial nerve palsy due to herpes zoster infection","Facial nerve paralysis due to VZV"],"definition":"A rare infectious disease characterized by herpes zoster oticus associated with peripheral facial nerve palsy, often also with other cranial nerve lesions. Patients present with a painful erythematous vesicular rash in and around one ear and facial paralysis on the same side. Other frequent manifestations include hearing loss, tinnitus, vertigo, nausea, vomiting, and nystagmus.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-3020/","orphanet_url":"https://www.orpha.net/en/disease/detail/3020","names":{"fr":{"name":"Syndrome de Ramsay Hunt","synonyms":["Paralysie faciale liée à l'infection par le VZV","Paralysie faciale liée à l'infection par le virus varicelle zona"],"definition":"Maladie infectieuse rare caractérisée par un zona auriculaire (herpès zoster oticus) associé à une paralysie périphérique du nerf facial, souvent accompagnée d'autres lésions des nerfs crâniens. Les patients manifestent une éruption vésiculaire érythémateuse douloureuse qui touche la partie externe et interne de l'oreille. et une paralysie faciale du même côté. Les autres signes cliniques fréquents sont la perte d'audition, les acouphènes, les vertiges, les nausées, les vomissements et le nystagmus."},"de":{"name":"Ramsay-Hunt-Syndrom","synonyms":["Fazialislähmung durch VZV","Fazialisparese Herpes zoster-Infektion","Fazialisparese durch Varicella-Zoster-Virus"],"definition":"Eine seltene Infektionskrankheit, die durch Herpes zoster oticus gekennzeichnet ist und mit einer peripheren Gesichtsnervenlähmung einhergeht, häufig auch mit anderen Hirnnervenläsionen. Die Patienten zeigen einen schmerzhaften, erythematösen, bläschenförmigen Ausschlag in und um ein Ohr und eine Gesichtslähmung auf der gleichen Seite. Zu den weiteren häufigen Symptomen gehören Hörverlust, Tinnitus, Schwindel, Übelkeit, Erbrechen und Nystagmus."},"es":{"name":"Síndrome de Ramsay Hunt","synonyms":["Parálisis del nervio facial por VZV","Parálisis del nervio facial por una infección por herpes zóster"],"definition":"Es una enfermedad infecciosa poco frecuente caracterizada por un herpes zóster ótico asociado a parálisis del nervio facial periférico y, a menudo, también a lesiones en otros pares craneales. Los pacientes presentan una erupción vesicular eritematosa dolorosa en y alrededor del pabellón auricular y con parálisis facial en ese lado. Otras manifestaciones frecuentes incluyen pérdida auditiva, tinnitus, vértigo, náuseas, vómitos y nistagmo."},"it":{"name":"Sindrome di Ramsay Hunt","synonyms":["Paralisi dei nervi facciali da VZV","Paralisi dei nervi facciali dovuta a infezione da herpes zoster"],"definition":"Si tratta di una malattia infettiva rara, caratterizzata da herpes zoster oticus con paralisi dei nervi facciali periferici, spesso associata alle lesioni degli altri nervi cranici. I pazienti presentano un'eruzione eritematosa vescicolare dolorosa all'interno e attorno ad un orecchio e la paralisi facciale omolaterale. Altri segni clinici comuni sono la sordità, gli acufeni, le vertigini, la nausea, il vomito e il nistagmo."},"nl":{"name":"Syndroom van Ramsay Hunt","synonyms":["Aangezichtsverlamming door VZV","Aangezichtsverlamming door herpes zoster-infectie","Verlamming van de gelaatszenuw door VZV"],"definition":"Een zeldzame infectieziekte, gekarakteriseerd door herpes zoster oticus geassocieerd met perifere facialisparalyse, en vaak ook met laesies van andere hersenzenuwen. Patiënten presenteren zich met pijnlijke erythemateuze vesiculaire huiduitslag in en rond één oor, en aangezichtsverlamming aan dezelfde zijde. Andere frequente manifestaties zijn onder meer gehoorverlies, tinnitus, vertigo, misselijkheid, braken, en nystagmus."},"pt":{"name":"Síndrome Ramsay-Hunt","synonyms":["Ataxia mioclónica"]},"pl":{"name":"Zespół Ramsaya Hunta","synonyms":["Półpasiec uszny","Porażenie nerwu twarzowego z powodu półpaśca","Porażenie nerwu twarzowego z powodu VZV"]},"cs":{"name":"Ramsay-Huntův syndrom","synonyms":["Obrna lícního nervu způsobená VZV","Obrna lícního nervu způsobená infekcí herpes zoster","Obrna nervus facialis způsobená VZV"]},"uk":{"name":"Синдром Рамзі Ханта","synonyms":["Параліч лицьового нерва внаслідок інфекції оперізувального герпесу","Параліч лицьового нерва внаслідок вірусного гепатиту В","Параліч лицьового нерва внаслідок VZV"],"definition":"A rare infectious disease characterized by herpes zoster oticus associated with peripheral facial nerve palsy, often also with other cranial nerve lesions. Patients present with a painful erythematous vesicular rash in and around one ear and facial paralysis on the same side. Other frequent manifestations include hearing loss, tinnitus, vertigo, nausea, vomiting, and nystagmus."},"zh":{"name":"拉姆齐·亨特综合征","synonyms":["带状疱疹感染所致面神经麻痹"]},"tr":{"name":"Ramsay Hunt sendromu","synonyms":["VZV'ye bağlı fasiyal sinir felci","VZV'ye bağlı fasiyal sinir paraliz","Herpes zoster enfeksiyonuna bağlı fasiyal sinir felci"]}},"xrefs":[{"source":"ICD-10","code":"B02.2+","qualifier":"NTBT","icd_relation":"index","validated":true},{"source":"ICD-10","code":"G53.0*","qualifier":"NTBT","icd_relation":"index","validated":true},{"source":"ICD-11","code":"8B88.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"305361524"},{"source":"MONDO","code":"0005769","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"5769","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0017409","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"7525","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[{"type":"Referred to","orpha":412220,"name":"OBSOLETE: Ramsay Hunt syndrome type II","status":"inactive"}],"preferential_parent":{"orpha":68416,"name":"Rare infectious disease"},"parents":[{"orpha":206613,"name":"Infectious disease with peripheral neuropathy","classifications":[181]},{"orpha":163585,"name":"Rare viral disease","classifications":[203]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":5.0,"area":"United States","status":"Validated","source":"23763077[PMID]_24799517[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}