raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:300912

Marginal zone lymphoma

Type
Clinical group
Group
Group of disorders
Age of onset
Adult
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enMarginal zone lymphoma
frLymphome de la zone marginale
deMarginalzonenlymphom
esLinfoma de la zona marginal
itLinfoma della zona marginale
nlMarginale zone lymfoom
ptLinfoma da zona marginal
plChłoniak strefy brzeżnej
csLymfom z buněk marginální zóny
ukЛімфома маргінальної зони
zh边缘区淋巴瘤
trMarjinal bölge lenfoması
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO0017604Evalidated
MONDO17604Evalidated
MeSHD018442Evalidated
UMLSC0242647Evalidated
GARD13237Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (4):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

3 records
TypeClassValueAreaQualificationValidationSource
Point prevalence1-9 / 100 0007 / 100 000EuropeValue and classValidatedEuropean Medicines Agency 2015[OTHER]
Annual incidence1-9 / 100 0002.8 / 100 000FranceValue and classValidatedOTHERitut National du Cancer 2013[OTHER]
Annual incidence1-9 / 1 000 0000.3 / 100 000EuropeValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card