{"orpha":300912,"name":"Marginal zone lymphoma","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-300912/","orphanet_url":"https://www.orpha.net/en/disease/detail/300912","names":{"fr":{"name":"Lymphome de la zone marginale"},"de":{"name":"Marginalzonenlymphom"},"es":{"name":"Linfoma de la zona marginal"},"it":{"name":"Linfoma della zona marginale"},"nl":{"name":"Marginale zone lymfoom"},"pt":{"name":"Linfoma da zona marginal"},"pl":{"name":"Chłoniak strefy brzeżnej"},"cs":{"name":"Lymfom z buněk marginální zóny"},"uk":{"name":"Лімфома маргінальної зони"},"zh":{"name":"边缘区淋巴瘤"},"tr":{"name":"Marjinal bölge lenfoması"}},"xrefs":[{"source":"MONDO","code":"0017604","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"17604","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D018442","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0242647","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"13237","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":300842,"name":"Indolent B-cell non-Hodgkin lymphoma","classifications":[194,202,233]}],"children":[{"orpha":52417,"name":"MALT lymphoma","type":"Disease"},{"orpha":86867,"name":"Nodal marginal zone B-cell lymphoma","type":"Disease"},{"orpha":300869,"name":"Splenic diffuse red pulp small B-cell lymphoma","type":"Disease"},{"orpha":86854,"name":"Splenic marginal zone lymphoma","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Value and class","class":"1-9 / 100 000","value":7.0,"area":"Europe","status":"Validated","source":"European Medicines Agency 2015[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":2.8,"area":"France","status":"Validated","source":"OTHERitut National du Cancer 2013[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.3,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"}],"phenotypes":null}