ORPHA:300903
ALK-negative anaplastic large cell lymphoma
Synonyms: ALK- ALCL · ALK- anaplastic large cell lymphoma
- Type
- Histopathological subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A type of ALCL, a rare and aggressive peripheral T-cell non-Hodgkin lymphoma affecting lymph nodes and extranodal sites, which is characterized by the lack of expression of a protein called anaplastic lymphoma kinase (ALK).
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | ALK-negative anaplastic large cell lymphoma | ALK- ALCL · ALK- anaplastic large cell lymphoma |
| fr | Lymphome anaplasique à grandes cellules ALK négatif | ALCL ALK- · LAGC ALK- · Lymphome anaplasique à grandes cellules ALK- |
| de | Lymphom, anaplastisches großzelliges, ALK-negatives | ALK-ALCL · ALK-anaplastisches großzelliges Lymphom |
| es | Linfoma anaplásico de células grandes ALK-negativo | ALK- ALCL · Linfoma anaplásico de células grandes ALK- |
| it | Linfoma anaplastico a grandi cellule ALK-negativo | ALK- ALCL · Linfoma anaplastico a grandi cellule ALK- |
| nl | ALK-negatief anaplastisch grootcellig lymfoom | ALK anaplastisch grootcellig lymfoom · ALK- ALCL |
| pt | Linfoma anaplásico de grandes células ALK - negativo | |
| pl | ALK-negatywny chłoniak anaplastyczny z dużych komórek | ALK- ALCL · ALK- chłoniak anaplastyczny z dużych komórek |
| cs | ALK-negativní anaplastický velkobuněčný lymfom | ALK- ALCL · ALK - anaplastický velkobuněčný lymfom |
| uk | ALK-негативна анапластична великоклітинна лімфома | ALK- ALCL · ALK - анапластична великоклітинна лімфома |
| zh | ALK阴性间变性大细胞淋巴瘤 | ALK间变性大细胞淋巴瘤 |
| tr | ALK negatif anaplastik büyük hücreli lenfoma | ALK- ALCL · ALK- anaplastik büyük hücreli lenfoma |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C84.7 | E | specific | validated |
| ICD-11 | 2A90.B | E | specific | validated |
| ICD-11 | XH9T74 | E | specific | validated |
| MONDO | 0017603 | E | validated | |
| UMLS | C1332078 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:98841Anaplastic large cell lymphoma
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/300903
- This record as JSON: /data/d/300903.json