ORPHA:284400
Small cell carcinoma of the bladder
Synonyms: Poorly differentiated neuroendocrine carcinoma of the bladder · SCCB · Small cell bladder cancer · Small cell bladder carcinoma · Small cell carcinoma of the urinary bladder
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
Small cell carcinoma of the bladder (SCCB) is a very rare, poorly differentiated neuroendocrine epithelial bladder tumor characterized clinically by hematuria and/or dysuria and a highly aggressive course.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Small cell carcinoma of the bladder | Poorly differentiated neuroendocrine carcinoma of the bladder · SCCB · Small cell bladder cancer · Small cell bladder carcinoma · Small cell carcinoma of the urinary bladder |
| fr | Carcinome à petites cellules de la vessie | Cancer à petites cellules de la vessie · Carcinome neuroendocrine primitif de la vessie · SCCB · Tumeur neuroendocrine à petites cellules de la vessie |
| de | Blasenkarzinom, kleinzelliges | Blasenkrebs, kleinzelliger · SCCB · Undifferenziertes neuroendokrines Blasenkarzinom |
| es | Carcinoma de células pequeñas de vejiga | Carcinoma de células pequeñas de la vejiga urinaria · Carcinoma de vejiga de células pequeñas · Carcinoma neuroendocrino pobremente diferenciado de la vejiga · Cáncer de vejiga de células pequeñas · SCCB |
| it | Carcinoma a piccole cellule della vescica | Cancro a piccole cellule della vescica · Carcinoma a piccole cellule della vescica urinaria · Carcinoma neuroendocrino scarsamente differenziato della vescica · SCCB |
| nl | Kleincellig carcinoom van blaas | Kleincellig blaascarcinoom · Kleincellig carcinoom van urineblaas · Kleincellige blaaskanker · SCCB · Slecht gedifferentieerd neuro-endocrien carcinoom van blaas |
| pt | Carcinoma das células pequenas da bexiga | |
| pl | Drobnokomórkowy rak pęcherza moczowego | Drobnokomórkowy nowotwór pęcherza moczowego · Nowotwór drobnokomórkowy pęcherzyka żółciowego · Rak drobnokomórkowy pęcherzyka żółciowego · SCCB · Słabo zróżnicowany neuroendokrynny rak pęcherza moczowego |
| cs | Malobuněčný karcinom močového měchýře | SCCB · Nediferencovaný neuroendokrinní karcinom močového měchýře · Malobuněčný zhoubný nádor močového měchýře |
| uk | Дрібноклітинний рак сечового міхура | Погано диференційована нейроендокринна карцинома сечового міхура · SCCB · Дрібноклітинний рак сечового міхура · Дрібноклітинна карцинома сечового міхура · Дрібноклітинний рак сечового міхура |
| zh | 膀胱小细胞癌 | 低分化膀胱神经内分泌癌 |
| tr | Mesanenin küçük hücreli karsinomu | SCCB · Küçük hücreli mesane kanseri · Küçük hücreli mesane karsinomu · Mesanenin küçük hücreli karsinomu · Mesanenin kötü diferansiye nöroendokrin karsinomu |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C67.0 | BTNT | attributed | validated |
| ICD-10 | C67.1 | BTNT | attributed | validated |
| ICD-10 | C67.2 | BTNT | attributed | validated |
| ICD-10 | C67.3 | BTNT | attributed | validated |
| ICD-10 | C67.4 | BTNT | attributed | validated |
| ICD-10 | C67.5 | BTNT | attributed | validated |
| ICD-10 | C67.6 | BTNT | attributed | validated |
| ICD-10 | C67.7 | BTNT | attributed | validated |
| ICD-10 | C67.8 | BTNT | attributed | validated |
| ICD-10 | C67.9 | BTNT | attributed | validated |
| ICD-11 | 2C13.Y | NTBT | attributed | validated |
| MONDO | 0004114 | E | validated | |
| MONDO | 4114 | E | validated | |
| UMLS | C1332564 | E | validated | |
| GARD | 11923 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:100101Neuroendocrine tumor with other location
rare endocrine diseases; rare neoplastic diseases - ORPHA:98058Rare urinary tract tumor
rare urogenital diseases; rare neoplastic diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
3 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | <1 / 1 000 000 | — | Europe | Class only | Not yet validated | ORPHANET |
| Annual incidence | <1 / 1 000 000 | — | Europe | Class only | Validated | [EXPERT] |
| Annual incidence | 1-9 / 1 000 000 | 0.14 / 100 000 | United States | Value and class | Validated | 21567387[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
6 annotations · validated 2016-06-01| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Very frequent (99-80%) | ||
| HP:0009725 | Bladder neoplasm | |
| HP:0000790 | Hematuria | |
| Frequent (79-30%) | ||
| HP:0100518 | Dysuria | |
| Occasional (29-5%) | ||
| HP:0002027 | Abdominal pain | |
| HP:0003072 | Hypercalcemia | |
| HP:0000010 | Recurrent urinary tract infections | |
Run the differential on the 2 obligate / very frequent terms
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/284400
- This record as JSON: /data/d/284400.json