raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:283

Demodicidosis

Synonyms: Demodicosis

Type
Disease
Group
Disorder
Status
active

Demodicidosis is a rare parasitic cutaneous disease due to <i>Demodex</i> mite infestation characterized by variable degrees of spinulosis, erythema, papules, and pustules, usually accompanied by a burning or pruritic sensation. Face (incl. eyelids) is most frequently affected, but ear canal, scalp, neck, back, chest, nipples, buttocks, penis, and extremity (legs and arms) involvement have also been observed. Dermoscopic examination reveals Demodex tails and follicular openings.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enDemodicidosisDemodicosis
frDémodécieDémodicidose · Démodécidose
deDemodikoseDemodicidosis
esDemodicidosis
itDemodicosi
nlDemodicoseDemodicidosis
ptDermodicidose
plDemodekoza= en
csDemodicidózaDemodikóza
ukДемодекозДемодекоз
zh蠕形螨病脂螨病
trDemodisidozDemodikoz

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10B88.0NTBTinclusionvalidated
ICD-111G07.0Especificvalidated
MONDO0017280Evalidated
UMLSC0392666Evalidated
GARD1802Evalidated
MedDRA10075310Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card