{"orpha":283,"name":"Demodicidosis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Demodicosis"],"definition":"Demodicidosis is a rare parasitic cutaneous disease due to <i>Demodex</i> mite infestation characterized by variable degrees of spinulosis, erythema, papules, and pustules, usually accompanied by a burning or pruritic sensation. Face (incl. eyelids) is most frequently affected, but ear canal, scalp, neck, back, chest, nipples, buttocks, penis, and extremity (legs and arms) involvement have also been observed. Dermoscopic examination reveals Demodex tails and follicular openings.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-283/","orphanet_url":"https://www.orpha.net/en/disease/detail/283","names":{"fr":{"name":"Démodécie","synonyms":["Démodicidose","Démodécidose"],"definition":"La démodécie est une maladie cutanée parasitaire causée par l'infestation par l'acarien <i>Demodex</i>, et caractérisée par des degrés variables de spinulosis, un érythème, des papules et des pustules, habituellement accompagnés par une sensation de brûlure et de prurit. Le visage (y compris les paupières) est le plus souvent affecté, mais le canal auditif, le cuir chevelu, le cou, le dos, le thorax, les mamelons, les fesses, le pénis et les extrémités (bras et jambes) peuvent aussi l'être. L'examen dermoscopique révèle des queues de Demodex et des ouvertures folliculaires."},"de":{"name":"Demodikose","synonyms":["Demodicidosis"],"definition":"Die Demodikose ist eine seltene parasitäre Hauterkrankung, die auf einen Befall mit <i>Demodex</i>-Milben zurückzuführen ist. Sie zeichnet sich durch unterschiedlich stark ausgeprägte erythematöse Papeln, Erytheme und Pusteln aus, die in der Regel mit einem brennenden oder juckenden Gefühl einhergehen. Das Gesicht (inkl. Augenlider) ist am häufigsten betroffen, aber auch Gehörgang, Kopfhaut, Nacken, Rücken, Brust, Brustwarzen, Gesäß, Penis und Extremitäten (Beine und Arme) wurden befallen. Die dermoskopische Untersuchung ermöglicht die Darstellung der saprophytären Besiedlung der Talgdrüsenfollikel (3-5 oder auch mehr Milben in einem ausgeweiteten Follikel)."},"es":{"name":"Demodicidosis","definition":"Es una enfermedad cutánea parasitaria poco frecuente debida a una infestación por ácaros <i>Demodex</i> caracterizada por grados variables de espinulosis, eritema, pápulas y pústulas, generalmente acompañada de una sensación de ardor o prurito. El rostro (incl. párpados) se ve afectado con mayor frecuencia, pero también se ha observado afectación del canal auditivo, cuero cabelludo, cuello, espalda, tórax, pezones, glúteos, pene y extremidades (piernas y brazos). El examen dermatoscópico revela colas de <i>Demodex</i> y aberturas foliculares."},"it":{"name":"Demodicosi","definition":"La demodicosi è una parassitosi cutanea rara causata dall'infestazione da acaro della specie Demodex. È caratterizzata da espressioni variabili di spinulosi, eritema, papule e pustole, di solito associate a bruciore o prurito. In genere il volto è più colpito (comprese le palpebre), ma la malattia può interessare anche il canale auricolare, il cuoio capelluto, il collo, la schiena, il torace, i capezzoli, le natiche, il pene e gli arti (gambe e braccia). La dermoscopia evidenzia la presenza di code di Demodex e aperture follicolari."},"nl":{"name":"Demodicose","synonyms":["Demodicidosis"],"definition":"Demodicose is een zeldzame parasitaire huidziekte als gevolg van infectie met <i>Demodex</i> haarfollikelmijt en wordt gekarakteriseerd door variabele gradaties van spinulosus, erytheem, papels, en puisten, meestal vergezeld door een brandend of jeukend gevoel. Het gelaat (incl. oogleden) wordt het meest frequent getroffen, maar betrokkenheid van de gehoorgang, hoofdhuid, nek/hals, rug, borst, tepels, zitvlak, penis, en ledematen (benen en armen) werd ook reeds waargenomen. Dermoscopisch onderzoek toont staarten van Demodex en folliculaire openingen."},"pt":{"name":"Dermodicidose"},"pl":{"name":"Demodekoza","synonyms":["Demodicosis"]},"cs":{"name":"Demodicidóza","synonyms":["Demodikóza"]},"uk":{"name":"Демодекоз","synonyms":["Демодекоз"],"definition":"Demodicidosis is a rare parasitic cutaneous disease due to <i>Demodex</i> mite infestation characterized by variable degrees of spinulosis, erythema, papules, and pustules, usually accompanied by a burning or pruritic sensation. Face (incl. eyelids) is most frequently affected, but ear canal, scalp, neck, back, chest, nipples, buttocks, penis, and extremity (legs and arms) involvement have also been observed. Dermoscopic examination reveals Demodex tails and follicular openings."},"zh":{"name":"蠕形螨病","synonyms":["脂螨病"]},"tr":{"name":"Demodisidoz","synonyms":["Demodikoz"]}},"xrefs":[{"source":"ICD-10","code":"B88.0","qualifier":"NTBT","icd_relation":"inclusion","validated":true},{"source":"ICD-11","code":"1G07.0","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1473144548"},{"source":"MONDO","code":"0017280","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0392666","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"1802","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10075310","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":68416,"name":"Rare infectious disease"},"parents":[{"orpha":163588,"name":"Rare parasitic disease","classifications":[203]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}