raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:280811

Extralobar congenital pulmonary sequestration

Synonyms: Congenital extrapulmonary sequestration · Extralobar congenital bronchopulmonary sequestration

Type
Clinical subtype
Group
Subtype of disorder
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enExtralobar congenital pulmonary sequestrationCongenital extrapulmonary sequestration · Extralobar congenital bronchopulmonary sequestration
frSéquestration pulmonaire congénitale extralobaireSéquestration broncho-pulmonaire congénitale extralobaire · Séquestration extrapulmonaire congénitale
deLungensequestration, extralobäre kongenitaleBronchopulmonale Sequestration, extralobäre kongenitale
esSecuestro pulmonar congénito extralobarSecuestro extrapulmonar congénito · Secuestro broncopulmonar congénito extralobar
itSequestro polmonare extralobare congenitoSequestro broncopolmonare extralobare congenito · Sequestro extrapolmonare congenito
nlExtralobair congenitaal longsekwesterCongenitale extrapulmonale sequestratie · Extralobaire congenitale bronchopulmonale sequestratie
ptSequestro pulmonar congénito extralobarSequestro broncopulmonar congénito extralobar · Sequestro extrapulmonar congénito
plWrodzona sekwestracja pozapłatowa płucWrodzona sekwestracja pozapłatowa oskrzelowo-płucna · Wrodzona sekwestracja pozapłucna
csVrozená extralobární plicní sekvestraceVrozená extrapulmonární sekvestrace · Extralobární vrozená bronchopulmonární sekvestrace
ukЕкстралобарна вроджена легенева секвестраціяВроджена позалегенева секвестрація · Екстралобарна вроджена бронхолегенева секвестрація
zh叶外先天性肺隔离症叶外先天性支气管肺隔离症
trEkstralobar Doğumsal pulmoner sekestrasyonDoğumsal ekstrapulmoner sekestrasyon · Ekstralobar doğumsal bronkopulmoner sekestrasyon
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10Q33.2NTBTattributedvalidated
ICD-11LA75.6NTBTindexvalidated
MONDO0017246Evalidated
UMLSC5679951Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card