ORPHA:280811
Extralobar congenital pulmonary sequestration
Synonyms: Congenital extrapulmonary sequestration · Extralobar congenital bronchopulmonary sequestration
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Extralobar congenital pulmonary sequestration | Congenital extrapulmonary sequestration · Extralobar congenital bronchopulmonary sequestration |
| fr | Séquestration pulmonaire congénitale extralobaire | Séquestration broncho-pulmonaire congénitale extralobaire · Séquestration extrapulmonaire congénitale |
| de | Lungensequestration, extralobäre kongenitale | Bronchopulmonale Sequestration, extralobäre kongenitale |
| es | Secuestro pulmonar congénito extralobar | Secuestro extrapulmonar congénito · Secuestro broncopulmonar congénito extralobar |
| it | Sequestro polmonare extralobare congenito | Sequestro broncopolmonare extralobare congenito · Sequestro extrapolmonare congenito |
| nl | Extralobair congenitaal longsekwester | Congenitale extrapulmonale sequestratie · Extralobaire congenitale bronchopulmonale sequestratie |
| pt | Sequestro pulmonar congénito extralobar | Sequestro broncopulmonar congénito extralobar · Sequestro extrapulmonar congénito |
| pl | Wrodzona sekwestracja pozapłatowa płuc | Wrodzona sekwestracja pozapłatowa oskrzelowo-płucna · Wrodzona sekwestracja pozapłucna |
| cs | Vrozená extralobární plicní sekvestrace | Vrozená extrapulmonární sekvestrace · Extralobární vrozená bronchopulmonární sekvestrace |
| uk | Екстралобарна вроджена легенева секвестрація | Вроджена позалегенева секвестрація · Екстралобарна вроджена бронхолегенева секвестрація |
| zh | 叶外先天性肺隔离症 | 叶外先天性支气管肺隔离症 |
| tr | Ekstralobar Doğumsal pulmoner sekestrasyon | Doğumsal ekstrapulmoner sekestrasyon · Ekstralobar doğumsal bronkopulmoner sekestrasyon |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | Q33.2 | NTBT | attributed | validated |
| ICD-11 | LA75.6 | NTBT | index | validated |
| MONDO | 0017246 | E | validated | |
| UMLS | C5679951 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:3161Congenital pulmonary sequestration
rare developmental anomalies during embryogenesis; rare respiratory diseases; rare surgical thoracic diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/280811
- This record as JSON: /data/d/280811.json