{"orpha":280811,"name":"Extralobar congenital pulmonary sequestration","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Congenital extrapulmonary sequestration","Extralobar congenital bronchopulmonary sequestration"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-280811/","orphanet_url":"https://www.orpha.net/en/disease/detail/280811","names":{"fr":{"name":"Séquestration pulmonaire congénitale extralobaire","synonyms":["Séquestration broncho-pulmonaire congénitale extralobaire","Séquestration extrapulmonaire congénitale"]},"de":{"name":"Lungensequestration, extralobäre kongenitale","synonyms":["Bronchopulmonale Sequestration, extralobäre kongenitale"]},"es":{"name":"Secuestro pulmonar congénito extralobar","synonyms":["Secuestro extrapulmonar congénito","Secuestro broncopulmonar congénito extralobar"]},"it":{"name":"Sequestro polmonare extralobare congenito","synonyms":["Sequestro broncopolmonare extralobare congenito","Sequestro extrapolmonare congenito"]},"nl":{"name":"Extralobair congenitaal longsekwester","synonyms":["Congenitale extrapulmonale sequestratie","Extralobaire congenitale bronchopulmonale sequestratie"]},"pt":{"name":"Sequestro pulmonar congénito extralobar","synonyms":["Sequestro broncopulmonar congénito extralobar","Sequestro extrapulmonar congénito"]},"pl":{"name":"Wrodzona sekwestracja pozapłatowa płuc","synonyms":["Wrodzona sekwestracja pozapłatowa oskrzelowo-płucna","Wrodzona sekwestracja pozapłucna"]},"cs":{"name":"Vrozená extralobární plicní sekvestrace","synonyms":["Vrozená extrapulmonární sekvestrace","Extralobární vrozená bronchopulmonární sekvestrace"]},"uk":{"name":"Екстралобарна вроджена легенева секвестрація","synonyms":["Вроджена позалегенева секвестрація","Екстралобарна вроджена бронхолегенева секвестрація"]},"zh":{"name":"叶外先天性肺隔离症","synonyms":["叶外先天性支气管肺隔离症"]},"tr":{"name":"Ekstralobar Doğumsal pulmoner sekestrasyon","synonyms":["Doğumsal ekstrapulmoner sekestrasyon","Ekstralobar doğumsal bronkopulmoner sekestrasyon"]}},"xrefs":[{"source":"ICD-10","code":"Q33.2","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"LA75.6","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"2043116979"},{"source":"MONDO","code":"0017246","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679951","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93890,"name":"Rare developmental defect during embryogenesis"},"parents":[{"orpha":3161,"name":"Congenital pulmonary sequestration","classifications":[147,184,186]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}