raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:280802

Intralobar congenital pulmonary sequestration

Synonyms: Congenital intrapulmonary sequestration · Intralobar congenital bronchopulmonary sequestration

Type
Clinical subtype
Group
Subtype of disorder
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enIntralobar congenital pulmonary sequestrationCongenital intrapulmonary sequestration · Intralobar congenital bronchopulmonary sequestration
frSéquestration pulmonaire congénitale intralobaireSéquestration broncho-pulmonaire congénitale intralobaire · Séquestration intrapulmonaire congénitale
deLungensequestration, intralobäre kongenitaleBronchopulmonale Sequestration, intralobäre kongenitale
esSecuestro pulmonar congénito intralobarSecuestro broncopulmonar congénito intralobar · Secuestro intrapulmonar congénito
itSequestro polmonare intralobare congenitoSequestro broncopolmonare intralobare congenito · Sequestro intrapolmonare congenito
nlIntralobair congenitaal longsekwesterCongenitale intrapulmonale sequestratie · Intralobaire congenitale bronchopulmonale sequestratie
ptSequestro pulmonar congénito intralobarSequestro broncopulmonar congénito intralobar · Sequestro intrapulmonar congénito
plWrodzona sekwestracja wewnątrzpłatowa płucWrodzona sekwestracja wewnątrzpłatowa oskrzelowo-płucna · Wrodzona sekwestracja wewnątrzpłucna
csVrozená intralobární plicní sekvestraceVrozená intrapulmonální sekvestrace · Intralobární vrozená bronchopulmonální sekvestrace
ukВнутрішньолобарна вроджена легенева секвестраціяВроджена внутрішньолегенева секвестрація · Внутрішньолобарна вроджена бронхолегенева секвестрація
zh叶内先天性肺隔离症叶内先天性支气管肺隔离症
trIntralobar Doğumsal pulmoner sekestrasyonDoğumsal intrapulmoner sekestrasyon · Intralobar doğumsal bronkopulmoner sekestrasyon
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10Q33.2NTBTattributedvalidated
ICD-11LA75.6NTBTindexvalidated
MONDO0017245Evalidated
UMLSC5679950Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card