{"orpha":280802,"name":"Intralobar congenital pulmonary sequestration","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Congenital intrapulmonary sequestration","Intralobar congenital bronchopulmonary sequestration"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-280802/","orphanet_url":"https://www.orpha.net/en/disease/detail/280802","names":{"fr":{"name":"Séquestration pulmonaire congénitale intralobaire","synonyms":["Séquestration broncho-pulmonaire congénitale intralobaire","Séquestration intrapulmonaire congénitale"]},"de":{"name":"Lungensequestration, intralobäre kongenitale","synonyms":["Bronchopulmonale Sequestration, intralobäre kongenitale"]},"es":{"name":"Secuestro pulmonar congénito intralobar","synonyms":["Secuestro broncopulmonar congénito intralobar","Secuestro intrapulmonar congénito"]},"it":{"name":"Sequestro polmonare intralobare congenito","synonyms":["Sequestro broncopolmonare intralobare congenito","Sequestro intrapolmonare congenito"]},"nl":{"name":"Intralobair congenitaal longsekwester","synonyms":["Congenitale intrapulmonale sequestratie","Intralobaire congenitale bronchopulmonale sequestratie"]},"pt":{"name":"Sequestro pulmonar congénito intralobar","synonyms":["Sequestro broncopulmonar congénito intralobar","Sequestro intrapulmonar congénito"]},"pl":{"name":"Wrodzona sekwestracja wewnątrzpłatowa płuc","synonyms":["Wrodzona sekwestracja wewnątrzpłatowa oskrzelowo-płucna","Wrodzona sekwestracja wewnątrzpłucna"]},"cs":{"name":"Vrozená intralobární plicní sekvestrace","synonyms":["Vrozená intrapulmonální sekvestrace","Intralobární vrozená bronchopulmonální sekvestrace"]},"uk":{"name":"Внутрішньолобарна вроджена легенева секвестрація","synonyms":["Вроджена внутрішньолегенева секвестрація","Внутрішньолобарна вроджена бронхолегенева секвестрація"]},"zh":{"name":"叶内先天性肺隔离症","synonyms":["叶内先天性支气管肺隔离症"]},"tr":{"name":"Intralobar Doğumsal pulmoner sekestrasyon","synonyms":["Doğumsal intrapulmoner sekestrasyon","Intralobar doğumsal bronkopulmoner sekestrasyon"]}},"xrefs":[{"source":"ICD-10","code":"Q33.2","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"LA75.6","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"500637990"},{"source":"MONDO","code":"0017245","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679950","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93890,"name":"Rare developmental defect during embryogenesis"},"parents":[{"orpha":3161,"name":"Congenital pulmonary sequestration","classifications":[147,184,186]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}