Pulmonary arterial hypertension associated with schistosomiasis
Synonyms: PAH associated with schistosomiasis
- Type
- Clinical group
- Group
- Group of disorders
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Pulmonary arterial hypertension associated with schistosomiasis (PAHS) is a form of pulmonary arterial hypertension characterized by an elevated pulmonary arterial resistance leading to right heart failure, observed as a complication of a chronic schistosomiasis.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Pulmonary arterial hypertension associated with schistosomiasis | PAH associated with schistosomiasis |
| fr | Hypertension artérielle pulmonaire associée à une schistosomiase | HTAP associée à une schistosomiase |
| de | Pulmonale arterielle Hypertonie mit assoziierter Schistosomiasis | PAH mit assoziierter Schistosomiasis |
| es | Hipertensión arterial pulmonar asociada a esquistosomiasis | HAP asociada a esquistosomiasis |
| it | Ipertensione arteriosa polmonare associata a schistosomiasi | PAH associata a schistosomiasi |
| nl | Pulmonale arteriële hypertensie geassocieerd met schistosomiase | PAH geassocieerd met schistosomiase |
| pt | Hipertensão arterial pulmonar associada a esquistossomose | |
| pl | Tętnicze nadciśnienie płucne związane z schistosomatozą | PAH związane z schistosomatozą |
| cs | Plicní arteriální hypertenze asociovaná se schistosomózou | PAH asociovaná se schistosomózou |
| uk | Легенева артеріальна гіпертензія, асоційована з шистосомозом | ЛАГ, повязана з шистосомозом |
| zh | 血吸虫病相关肺动脉高压 | 血吸虫病相关PAH |
| tr | Şistosomiaz ilişkili pulmoner arteriyel hipertansiyon | Şistozomiyaz ile ilişkili PAH |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 17155 | E | validated | |
| UMLS | C3697477 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:275791Pulmonary arterial hypertension associated with another disease
rare respiratory diseases; rare transplant-related disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/275823
- This record as JSON: /data/d/275823.json