{"orpha":275823,"name":"Pulmonary arterial hypertension associated with schistosomiasis","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["PAH associated with schistosomiasis"],"definition":"Pulmonary arterial hypertension associated with schistosomiasis (PAHS) is a form of pulmonary arterial hypertension characterized by an elevated pulmonary arterial resistance leading to right heart failure, observed as a complication of a chronic schistosomiasis.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-275823/","orphanet_url":"https://www.orpha.net/en/disease/detail/275823","names":{"fr":{"name":"Hypertension artérielle pulmonaire associée à une schistosomiase","synonyms":["HTAP associée à une schistosomiase"],"definition":"Forme d'hypertension artérielle pulmonaire caractérisée par une résistance artérielle pulmonaire élevée entraînant une insuffisance cardiaque droite, observée comme complication d'une schistosomiase chronique."},"de":{"name":"Pulmonale arterielle Hypertonie mit assoziierter Schistosomiasis","synonyms":["PAH mit assoziierter Schistosomiasis"]},"es":{"name":"Hipertensión arterial pulmonar asociada a esquistosomiasis","synonyms":["HAP asociada a esquistosomiasis"],"definition":"La hipertensión arterial pulmonar asociada a la esquistosomiasis (PAHS; por sus siglas en inglés) es una forma de hipertensión arterial pulmonar (HAP) caracterizada por una resistencia arterial pulmonar elevada que conduce a insuficiencia cardíaca derecha, observada como una complicación de la esquistosomiasis crónica."},"it":{"name":"Ipertensione arteriosa polmonare associata a schistosomiasi","synonyms":["PAH associata a schistosomiasi"]},"nl":{"name":"Pulmonale arteriële hypertensie geassocieerd met schistosomiase","synonyms":["PAH geassocieerd met schistosomiase"],"definition":"'Pulmonale arteriële hypertensie geassocieerd met schistosomiase (PAHS) is een vorm van pulmonale arteriële hypertensie (PAH; zie deze term) die wordt gekarakteriseerd door een verhoogde weerstand in de longslagaders die wordt waargenomen als een complicatie van chronische schistosomiase (zie deze term) en die leidt tot een falen van de rechterzijde van het hart.'"},"pt":{"name":"Hipertensão arterial pulmonar associada a esquistossomose"},"pl":{"name":"Tętnicze nadciśnienie płucne związane z schistosomatozą","synonyms":["PAH związane z schistosomatozą"]},"cs":{"name":"Plicní arteriální hypertenze asociovaná se schistosomózou","synonyms":["PAH asociovaná se schistosomózou"]},"uk":{"name":"Легенева артеріальна гіпертензія, асоційована з шистосомозом","synonyms":["ЛАГ, повязана з шистосомозом"],"definition":"Pulmonary arterial hypertension associated with schistosomiasis (PAHS) is a form of pulmonary arterial hypertension (see this term) characterized by an elevated pulmonary arterial resistance leading to right heart failure, observed as a complication of a chronic schistosomiasis (see this term)."},"zh":{"name":"血吸虫病相关肺动脉高压","synonyms":["血吸虫病相关PAH"],"definition":"血吸虫病相关肺动脉高压(PAHs)是一种肺动脉高压(见该词条)，其特征是肺动脉阻力升高导致右心衰竭，被认为是慢性血吸虫病(见该词条)的并发症。"},"tr":{"name":"Şistosomiaz ilişkili pulmoner arteriyel hipertansiyon","synonyms":["Şistozomiyaz ile ilişkili PAH"]}},"xrefs":[{"source":"MONDO","code":"17155","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C3697477","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97955,"name":"Rare respiratory disease"},"parents":[{"orpha":275791,"name":"Pulmonary arterial hypertension associated with another disease","classifications":[184,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}