ORPHA:275808
Pulmonary arterial hypertension associated with HIV infection
Synonyms: PAH associated with HIV infaction
- Type
- Clinical group
- Group
- Group of disorders
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A form of pulmonary arterial hypertension characterized by elevated pulmonary arterial resistance leading to right heart failure observed as a complication of HIV infection.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Pulmonary arterial hypertension associated with HIV infection | PAH associated with HIV infaction |
| fr | Hypertension artérielle pulmonaire associée à une infection VIH | HTAP associée à une infection VIH |
| de | Pulmonale arterielle Hypertonie mit assoziierter HIV-Infektion | PAH mit assoziierter HIV-Infektion |
| es | Hipertensión arterial pulmonar asociada con infección por VIH | HAP asociada a infección por VIH |
| it | Ipertensione arteriosa polmonare associata a infezione da HIV | PAH associata a infezione da HIV |
| nl | Pulmonale arteriële hypertensie geassocieerd met HIV-infectie | PAH geassocieerd met HIV-infectie |
| pt | Hipertensão arterial pulmonar associada à infecção pelo HIV | |
| pl | Tętnicze nadciśnienie płucne związane z zakażeniem HIV | PAH związane z zakażeniem HIV |
| cs | Plicní arteriální hypertenze asociovaná s HIV infekcí | PAH asociovaná s HIV infekcí |
| uk | Легенева артеріальна гіпертензія, асоційована з ВІЛ-інфекцією | ЛАГ, асоційована з ВІЛ-інфекцією |
| zh | HIV感染相关肺动脉高压 | HIV感染相关性PAH |
| tr | HIV enfeksiyonu ilişkili pulmoner arteriyel hipertansiyon | HIV enfeksiyonu ile ilişkili PAH |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 17153 | E | validated | |
| UMLS | C3697673 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:275791Pulmonary arterial hypertension associated with another disease
rare respiratory diseases; rare transplant-related disorders
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/275808
- This record as JSON: /data/d/275808.json