{"orpha":275808,"name":"Pulmonary arterial hypertension associated with HIV infection","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["PAH associated with HIV infaction"],"definition":"A form of pulmonary arterial hypertension characterized by elevated pulmonary arterial resistance leading to right heart failure observed as a complication of HIV infection.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-275808/","orphanet_url":"https://www.orpha.net/en/disease/detail/275808","names":{"fr":{"name":"Hypertension artérielle pulmonaire associée à une infection VIH","synonyms":["HTAP associée à une infection VIH"],"definition":"Forme d'hypertension artérielle pulmonaire caractérisée par une résistance artérielle pulmonaire élevée entraînant une insuffisance cardiaque droite observée comme complication de l'infection par le VIH."},"de":{"name":"Pulmonale arterielle Hypertonie mit assoziierter HIV-Infektion","synonyms":["PAH mit assoziierter HIV-Infektion"],"definition":"Eine Form der pulmonalen arteriellen Hypertonie, die durch einen erhöhten pulmonalen arteriellen Widerstand gekennzeichnet ist und zu Rechtsherzversagen führt, das als Komplikation einer HIV-Infektion beobachtet wird."},"es":{"name":"Hipertensión arterial pulmonar asociada con infección por VIH","synonyms":["HAP asociada a infección por VIH"],"definition":"Es una forma de hipertensión arterial pulmonar (HAP) caracterizada por resistencia arterial pulmonar elevada que conduce a insuficiencia cardíaca derecha observada como una complicación de la infección por VIH."},"it":{"name":"Ipertensione arteriosa polmonare associata a infezione da HIV","synonyms":["PAH associata a infezione da HIV"]},"nl":{"name":"Pulmonale arteriële hypertensie geassocieerd met HIV-infectie","synonyms":["PAH geassocieerd met HIV-infectie"],"definition":"Een vorm van pulmonale arteriële hypertensie (PAH), gekenmerkt door verhoogde weerstand in longslagaders die leidt tot rechterhartfalen, en waargenomen als complicatie van HIV-infectie."},"pt":{"name":"Hipertensão arterial pulmonar associada à infecção pelo HIV"},"pl":{"name":"Tętnicze nadciśnienie płucne związane z zakażeniem HIV","synonyms":["PAH związane z zakażeniem HIV"]},"cs":{"name":"Plicní arteriální hypertenze asociovaná s HIV infekcí","synonyms":["PAH asociovaná s HIV infekcí"]},"uk":{"name":"Легенева артеріальна гіпертензія, асоційована з ВІЛ-інфекцією","synonyms":["ЛАГ, асоційована з ВІЛ-інфекцією"],"definition":"A form of pulmonary arterial hypertension characterized by elevated pulmonary arterial resistance leading to right heart failure observed as a complication of HIV infection."},"zh":{"name":"HIV感染相关肺动脉高压","synonyms":["HIV感染相关性PAH"],"definition":"与HIV感染相关的肺动脉高压(PAH-HIV)是一种肺动脉高压，其特征是肺动脉阻力升高导致右心衰竭，被认为是HIV感染的并发症。"},"tr":{"name":"HIV enfeksiyonu ilişkili pulmoner arteriyel hipertansiyon","synonyms":["HIV enfeksiyonu ile ilişkili PAH"]}},"xrefs":[{"source":"MONDO","code":"17153","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C3697673","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97955,"name":"Rare respiratory disease"},"parents":[{"orpha":275791,"name":"Pulmonary arterial hypertension associated with another disease","classifications":[184,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}