raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:2700

Noma

Synonyms: Cancrum oris

Type
Disease
Group
Disorder
Age of onset
Childhood
Status
active

An orofacial gangrenous disease characterized by the rapid, severe destruction of the soft and osseous tissues of the face.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enNomaCancrum oris
frNomaStomatite nécrosante
deNoma= en
esNoma= en
itNoma
nlNoma= en
ptNoma
plNomaRak wodny
csNoma= en
ukНома= en
zh走马疳坏疽性溃疡口炎
trNomaKankrum oris

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10A69.0Especificvalidated
ICD-11DA0C.31Especificvalidated
MONDO0017124Evalidated
MeSHD009625Evalidated
UMLSC0028271Evalidated
GARD4001Evalidated
MedDRA10029502Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card