{"orpha":2700,"name":"Noma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Cancrum oris"],"definition":"An orofacial gangrenous disease characterized by the rapid, severe destruction of the soft and osseous tissues of the face.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-2700/","orphanet_url":"https://www.orpha.net/en/disease/detail/2700","names":{"fr":{"name":"Noma","synonyms":["Stomatite nécrosante"],"definition":"Maladie gangréneuse orofaciale caractérisée par une destruction rapide et importante des tissus mous et osseux de la face."},"de":{"name":"Noma","synonyms":["Cancrum oris"],"definition":"Eine orofaziale gangränöse Erkrankung, die durch eine rasche, schwere Zerstörung des weichen und knöchernen Gewebes des Gesichts gekennzeichnet ist."},"es":{"name":"Noma","synonyms":["Cancrum oris"],"definition":"Es una enfermedad gangrenosa orofacial caracterizada por la destrucción rápida y grave de los tejidos blandos y óseos de la cara."},"it":{"name":"Noma"},"nl":{"name":"Noma","synonyms":["Cancrum oris"],"definition":"Een orofaciale gangreneuze aandoening, gekenmerkt door snelle, ernstige destructie van weke delen en botweefsel van het aangezicht."},"pt":{"name":"Noma"},"pl":{"name":"Noma","synonyms":["Rak wodny"]},"cs":{"name":"Noma","synonyms":["Cancrum oris"]},"uk":{"name":"Нома","synonyms":["Cancrum oris"],"definition":"Noma is a gangrenous disease that causes severe destruction of the soft and osseous tissues of the face."},"zh":{"name":"走马疳","synonyms":["坏疽性溃疡口炎"]},"tr":{"name":"Noma","synonyms":["Kankrum oris"]}},"xrefs":[{"source":"ICD-10","code":"A69.0","qualifier":"E","icd_relation":"specific","validated":true},{"source":"ICD-11","code":"DA0C.31","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"340823130"},{"source":"MONDO","code":"0017124","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D009625","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0028271","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"4001","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10029502","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":68416,"name":"Rare infectious disease"},"parents":[{"orpha":163582,"name":"Rare bacterial infectious disease","classifications":[203]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Childhood"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}