ORPHA:264683
Primary interstitial lung disease specific to childhood due to alveolar vascular disorder
Synonyms: Primary ILD specific to childhood due to alveolar vascular disorder
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary interstitial lung disease specific to childhood due to alveolar vascular disorder | Primary ILD specific to childhood due to alveolar vascular disorder |
| fr | Pneumopathie interstitielle primaire spécifique de l'enfance due à une anomalie vasculaire des alvéoles | ILD primaire spécifique de l'enfance due à une anomalie vasculaire des alvéoles |
| de | Interstitielle Lungenkrankheit durch alveoläre Vaskulationsstörungen, primäre spezifische, der Kindheit | Primäre ILD der Kindheit durch alveoläre Vaskulationsstörungen |
| es | Enfermedad pulmonar intersticial primaria específica de la infancia por un trastorno vascular alveolar | EPI primaria específica de la infancia por un trastorno vascular alveolar |
| it | Pneumopatia interstiziale primitiva specifica dell'infanzia da anomalia vascolare degli alveoli | ILD primitiva specifica dell'infanzia da anomalia vascolare degli alveoli |
| nl | Primaire interstitiële longziekte specifiek voor de kinderjaren door alveolaire vasculaire stoornis | Primaire ILD specifiek voor de kinderjaren door alveolaire vasculaire stoornis |
| pt | Doença pulmonar intersticial primária específica da infância por doença vascular alveolar | |
| pl | Pierwotna śródmiąższowa choroba płuc specyficzna dla wieku dziecięcego z powodu zaburzeń naczyniowych pęcherzyków | Pierwotna ILD specyficzna dla wieku dziecięcego z powodu zaburzeń naczyniowych pęcherzyków |
| cs | Primární intersticiální plicní nemoc specifická pro dětství způsobená alveolární vaskulární poruchou | Primární ILD specifická pro dětství způsobená alveolární vaskulární poruchou |
| uk | Первинне інтерстиціальне захворювання легень, характерне для дитячого віку, повязане з альвеолярними судинними розладами | Первинна ILD, специфічна для дитячого віку, зумовлена альвеолярним судинним ураженням |
| zh | 肺泡血管疾病所致儿童期特有的原发性间质性肺病 | 肺泡血管疾病所致儿童期特有的原发性ILD |
| tr | Alveolar vasküler bozukluğa bağlı çocukluk çağı primer interstisyel akciğer hastalığı | Alveolar vasküler bozukluğa bağlı çocukluğa özgü primer ILD |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 17017 | E | validated | |
| UMLS | C5679755 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:264665Primary interstitial lung disease specific to childhood
rare respiratory diseases; rare transplant-related disorders
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/264683
- This record as JSON: /data/d/264683.json