ORPHA:254492
Frontal fibrosing alopecia
Synonyms: FFA
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adult
- Status
- active
Frontal fibrosing alopecia (FFA) is a rare variant of lichen planopilaris characterized by symmetrical, progressive, band-like anterior hair loss of the scalp.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Frontal fibrosing alopecia | FFA |
| fr | Alopécie frontale fibrosante | = en |
| de | Alopezie, fibrosierende frontale | = en |
| es | Alopecia frontal fibrosante | = en |
| it | Alopecia fibrosante frontale | = en |
| nl | Frontale fibroserende alopecie | = en |
| pt | Alopecia fibrosante frontal | = en |
| pl | Łysienie czołowe włókniejące | = en |
| cs | Frontální fibrotizující alopecie | = en |
| uk | Фронтальна фіброзна алопеція | = en |
| zh | 前额纤维性脱发 | = en |
| tr | Frontal fibrozan alopesi | = en |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L66.1 | NTBT | attributed | validated |
| ICD-11 | EA91.2 | NTBT | index | validated |
| MONDO | 0016776 | E | validated | |
| UMLS | C4255374 | E | validated | |
| GARD | 10886 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:79364Alopecia
rare skin diseases - ORPHA:254370Rare cutaneous lichen planus
rare skin diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/254492
- This record as JSON: /data/d/254492.json