{"orpha":254492,"name":"Frontal fibrosing alopecia","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["FFA"],"definition":"Frontal fibrosing alopecia (FFA) is a rare variant of lichen planopilaris characterized by symmetrical, progressive, band-like anterior hair loss of the scalp.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-254492/","orphanet_url":"https://www.orpha.net/en/disease/detail/254492","names":{"fr":{"name":"Alopécie frontale fibrosante","synonyms":["FFA"],"definition":"L'alopécie frontale fibrosante (AFF) est une variante rare de lichen plan pilaire (LPP) caractérisée par une alopécie frontale en bandes, symétrique et progressive."},"de":{"name":"Alopezie, fibrosierende frontale","synonyms":["FFA"],"definition":"Die Frontale fibrosierende Alopezie (FFA) ist eine seltene Variante des Lichen planopilaris (s. dort) und gekennzeichnet durch symmetrischen, progredienten, bandförmigen Haarverlust im vorderen Bereich der Kopfhaut."},"es":{"name":"Alopecia frontal fibrosante","synonyms":["FFA"],"definition":"La alopecia frontal fibrosante (FFA) es una variante poco frecuente del liquen plano pilar (consulte este término) que se caracteriza por una pérdida progresiva simétrica en forma de banda del pelo del cuero cabelludo."},"it":{"name":"Alopecia fibrosante frontale","synonyms":["FFA"],"definition":"L'alopecia fibrosante frontale (FFA) è una variante rara del lichen piano pilare (si veda questo termine), caratterizzata dalla perdita simmetrica e progressiva dei capelli, che si verifica a bande sulla parte anteriore del cuoio capelluto."},"nl":{"name":"Frontale fibroserende alopecie","synonyms":["FFA"],"definition":"Frontale fibroserende alopecie (FFA) is een zeldzame variant van lichen planopilaris (zie deze term) gekenmerkt door symmetrisch, progressief, band-achtig anterieur haarverlies van de hoofdhuid."},"pt":{"name":"Alopecia fibrosante frontal","synonyms":["FFA"],"definition":"A alopécia fibrosante frontal (FFA) é uma variante rara de líquen planopilar (ver este termo), caracterizada por perda de cabelo em banda na região anterior, simétrica e progressiva."},"pl":{"name":"Łysienie czołowe włókniejące","synonyms":["FFA"]},"cs":{"name":"Frontální fibrotizující alopecie","synonyms":["FFA"]},"uk":{"name":"Фронтальна фіброзна алопеція","synonyms":["FFA"],"definition":"Frontal fibrosing alopecia (FFA) is a rare variant of lichen planopilaris (see this term) characterized by symmetrical, progressive, band-like anterior hair loss of the scalp."},"zh":{"name":"前额纤维性脱发","synonyms":["FFA"],"definition":"额部纤维性脱发(FFA)是一种罕见的扁平苔藓变种，其特征是前部头皮呈对称性、进行性、带状脱发。"},"tr":{"name":"Frontal fibrozan alopesi","synonyms":["FFA"]}},"xrefs":[{"source":"ICD-10","code":"L66.1","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EA91.2","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1257078333"},{"source":"MONDO","code":"0016776","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4255374","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"10886","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":79364,"name":"Alopecia","classifications":[187]},{"orpha":254370,"name":"Rare cutaneous lichen planus","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}