raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:254463

Lichen planus pigmentosus

Synonyms: LP pigmentosa · LP pigmentosus · Lichen planus pigmentosa · Lichen planus pigmentosus inversus

Type
Disease
Group
Disorder
Age of onset
Adult
Status
active

Lichen planus (LP) pigmentosus is a rare variant of cutaneous lichen planus characterized by the presence of hyperpigmented lichenoid lesions in sun-exposed or flexural areas of the body.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enLichen planus pigmentosusLP pigmentosa · LP pigmentosus · Lichen planus pigmentosa · Lichen planus pigmentosus inversus
frLichen plan pigmentogèneLichen plan pigmentaire · Lichen plan pigmentaire et inversé · Lichen plan pigmentogène inversé · Lichen plan pigmentosa · Lichen plan pigmentosus · LP pigmentaire · LP pigmentosa · LP pigmentosus
deLichen planus pigmentosusLP pigmentosa · LP, pigmentöser · Lichen planus pigmentosus inversus
esLiquen plano pigmentosoLP pigmentosa · LP pigmentoso · Liquen plano pigmentoso inverso
itLichen planus pigmentosoLP pigmentoso · Lichen planus pigmentosus inversus
nlLichen planus pigmentosusGepigmenteerde lichen planus · LP pigmentosa · LP pigmentosus · Lichen planus pigmentosa · Lichen planus pigmentosus inversus
ptLíquen plano pigmentosoLP pigmentosa · LP pigmentoso · Líquen plano pigmentoso
plLiszaj płaski barwnikowyLiszaj płaski barwnikowy odwrócony · LP barwnikowy
csLichen planus pigmentosus= en
ukПігментний плескатий лишайЧервоний плоский лишай пігментний · Червоний плоский лишай (Lichenus planus pigmentosus inversus) · Пігментний LP · LP pigmentosus
zh色素性扁平苔藓色素性倒向扁平苔藓
trLiken planus pigmentozusLP pigmentoza · LP pigmentoz · Liken planus pigmentosa · Liken planus pigmentosus inversus

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10L43.8NTBTattributedvalidated
ICD-11EA91.YNTBTindexvalidated
MONDO0016774Evalidated
UMLSC0406366Evalidated
GARD10816Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card