{"orpha":254463,"name":"Lichen planus pigmentosus","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["LP pigmentosa","LP pigmentosus","Lichen planus pigmentosa","Lichen planus pigmentosus inversus"],"definition":"Lichen planus (LP) pigmentosus is a rare variant of cutaneous lichen planus characterized by the presence of hyperpigmented lichenoid lesions in sun-exposed or flexural areas of the body.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-254463/","orphanet_url":"https://www.orpha.net/en/disease/detail/254463","names":{"fr":{"name":"Lichen plan pigmentogène","synonyms":["Lichen plan pigmentaire","Lichen plan pigmentaire et inversé","Lichen plan pigmentogène inversé","Lichen plan pigmentosa","Lichen plan pigmentosus","LP pigmentaire","LP pigmentosa","LP pigmentosus"],"definition":"Le lichen plan (LP) pigmentogène est une variante rare de LP cutané caractérisée par la présence de lésions lichéniennes hyperpigmentées dans les zones photo-exposées ou dans les plis de flexion."},"de":{"name":"Lichen planus pigmentosus","synonyms":["LP pigmentosa","LP, pigmentöser","Lichen planus pigmentosus inversus"],"definition":"Der Lichen planus (LP) pigmentosus ist eine seltene Variante des kutanen Lichen planus (s. dort) und gekennzeichnet durch hyperpigmentierte lichenoide Läsionen in sonnenexponierten Bereichen und Hautfurchen."},"es":{"name":"Liquen plano pigmentoso","synonyms":["LP pigmentosa","LP pigmentoso","Liquen plano pigmentoso inverso"],"definition":"El liquen plano (LP) pigmentoso es una variante rara del liquen plano cutáneo (consulte este término) caracterizado por la presencia de lesiones liquenoides hiperpigmentadas en áreas del cuerpo expuestas al sol o de flexión."},"it":{"name":"Lichen planus pigmentoso","synonyms":["LP pigmentoso","Lichen planus pigmentosus inversus"],"definition":"Il lichen piano (LP) pigmentoso è una variante rara del lichen piano cutaneo (si veda questo termine), caratterizzata dalla presenza di lesioni lichenoidi iperpigmentate nelle aree del corpo esposte al sole o nelle pieghe di flessione."},"nl":{"name":"Lichen planus pigmentosus","synonyms":["Gepigmenteerde lichen planus","LP pigmentosa","LP pigmentosus","Lichen planus pigmentosa","Lichen planus pigmentosus inversus"],"definition":"Lichen planus (LP) pigmentosus is een zeldzame variant van cutane lichen planus (zie deze term) gekenmerkt door de aanwezigheid van hypergepigmenteerde lichenoïde laesies op aan de zon blootgestelde of flexurale lichaamszones."},"pt":{"name":"Líquen plano pigmentoso","synonyms":["LP pigmentosa","LP pigmentoso","Líquen plano pigmentoso"],"definition":"O líquen plano (LP) pigmentoso é uma variante rara de líquen plano cutâneo (ver este termo), caracterizado pela presença de lesões hiperpigmentadas liquenóides nas áreas do corpo expostas ao sol ou de flexão."},"pl":{"name":"Liszaj płaski barwnikowy","synonyms":["Liszaj płaski barwnikowy odwrócony","LP barwnikowy"]},"cs":{"name":"Lichen planus pigmentosus","synonyms":["LP pigmentosa","LP pigmentosus","Lichen planus pigmentosa","Lichen planus pigmentosus inversus"]},"uk":{"name":"Пігментний плескатий лишай","synonyms":["Червоний плоский лишай пігментний","Червоний плоский лишай (Lichenus planus pigmentosus inversus)","Пігментний LP","LP pigmentosus"],"definition":"Lichen planus (LP) pigmentosus is a rare variant of cutaneous lichen planus (see this term) characterized by the presence of hyperpigmented lichenoid lesions in sun-exposed or flexural areas of the body."},"zh":{"name":"色素性扁平苔藓","synonyms":["色素性倒向扁平苔藓"],"definition":"色素性扁平苔藓(LP)是一种罕见的皮肤扁平苔藓变种(见该词条)，其特征是在阳光暴露下或身体屈曲部位出现色素沉着的苔藓样病变。"},"tr":{"name":"Liken planus pigmentozus","synonyms":["LP pigmentoza","LP pigmentoz","Liken planus pigmentosa","Liken planus pigmentosus inversus"]}},"xrefs":[{"source":"ICD-10","code":"L43.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EA91.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1235685123"},{"source":"MONDO","code":"0016774","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0406366","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"10816","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":254370,"name":"Rare cutaneous lichen planus","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}