ORPHA:254411

Annular atrophic lichen planus

Synonyms: Annular atrophic LP

A rare variant of cutaneous lichen planus characterized by both annular and atrophic LP features in the same lesion.

Names in Orphadata languages

12 of 12 languages

Lang	Name	Synonyms
en	Annular atrophic lichen planus	Annular atrophic LP
fr	Lichen plan annulaire atrophique	LP annulaire atrophique
de	Anulärer atrophischer Lichen planus	Atrophischer Lichen planus anularis
es	Liquen plano anular atrófico
it	Lichen planus atrofico anulare	LP atrofico anulare
nl	Annulaire atrofische lichen planus	Annulaire atrofische LP · Ringvormige atrofische lichen planus
pt	Líquen plano atrófico anular	LP atrófico anular
pl	Liszaj płaski pierścieniowy zanikowy	LP pierścieniowy zanikowy
cs	Anulární atrofický lichen planus	Anulární atrofický LP
uk	Кільцеподібний атрофічний плескатий лишай	Кільцева атрофічна LP
zh	环状萎缩性扁平苔藓	环状萎缩性LP
tr	Halka şeklindeki atrofik liken planus	Annular atrofik LP

Definition in:

qualifier = Orphanet mapping relation

Source	Code	Qualifier	ICD relation	Validation
ICD-10	L43.8	NTBT	attributed	validated
ICD-11	EA91.Y	NTBT	attributed	validated
MONDO	0016771	E		validated
UMLS	C4304037	E		validated
GARD	12676	E		validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

0 direct

Orphanet records no gene directly on this code.

2 records

Type	Class	Value	Area	Qualification	Validation	Source
Cases/families		10 cases	Worldwide	Case(s)	Validated	[EXPERT]
Point prevalence	<1 / 1 000 000	—	Worldwide	Class only	Validated	ORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

Orphanet has no HPO annotation for this code in this release.