{"orpha":254411,"name":"Annular atrophic lichen planus","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Annular atrophic LP"],"definition":"A rare variant of cutaneous lichen planus characterized by both annular and atrophic LP features in the same lesion.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-254411/","orphanet_url":"https://www.orpha.net/en/disease/detail/254411","names":{"fr":{"name":"Lichen plan annulaire atrophique","synonyms":["LP annulaire atrophique"],"definition":"Variante rare du lichen plan (LP) cutané caractérisée par des signes à la fois de LP annulaire et de LP atrophique dans une même lésion."},"de":{"name":"Anulärer atrophischer Lichen planus","synonyms":["Atrophischer Lichen planus anularis"],"definition":"Der Anuläre atrophische Lichen planus (LP) ist eine seltene Variante des kutanen Lichen planus (s. dort) und gekennzeichnet durch Merkmale sowohl des anulären als auch des atrophischen LP in der gleichen Läsion."},"es":{"name":"Liquen plano anular atrófico","definition":"Es una variante poco frecuente del liquen plano (LP) cutáneo caracterizada por rasgos de LP anular y atrófico en una misma lesión."},"it":{"name":"Lichen planus atrofico anulare","synonyms":["LP atrofico anulare"],"definition":"Il lichen piano (LP) atrofico anulare è una variante rara del lichen piano cutaneo (si veda questo termine), caratterizzata dalla presenza dei segni del LP anulare e del lichen atrofico (si vedano questi termini) nella stessa lesione."},"nl":{"name":"Annulaire atrofische lichen planus","synonyms":["Annulaire atrofische LP","Ringvormige atrofische lichen planus"],"definition":"Een zeldzame variant van cutane lichen planus, gekarakteriseerd door kenmerken van zowel annulaire als atrofische LP in dezelfde laesie."},"pt":{"name":"Líquen plano atrófico anular","synonyms":["LP atrófico anular"],"definition":"Variante rara do líquen plano cutâneo, com características anulares e atróficas na mesma lesão."},"pl":{"name":"Liszaj płaski pierścieniowy zanikowy","synonyms":["LP pierścieniowy zanikowy"]},"cs":{"name":"Anulární atrofický lichen planus","synonyms":["Anulární atrofický LP"]},"uk":{"name":"Кільцеподібний атрофічний плескатий лишай","synonyms":["Кільцева атрофічна LP"],"definition":"A rare variant of cutaneous lichen planus characterized by both annular and atrophic LP features in the same lesion."},"zh":{"name":"环状萎缩性扁平苔藓","synonyms":["环状萎缩性LP"],"definition":"一种罕见的皮肤扁平苔藓变种，在同一处皮损中同时具有环状和萎缩性扁平苔藓的表现。"},"tr":{"name":"Halka şeklindeki atrofik liken planus","synonyms":["Annular atrofik LP"]}},"xrefs":[{"source":"ICD-10","code":"L43.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EA91.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true,"icd11_uri":"null"},{"source":"MONDO","code":"0016771","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4304037","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"12676","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":254370,"name":"Rare cutaneous lichen planus","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":10.0,"area":"Worldwide","status":"Validated","source":"[EXPERT]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}